Clinical Rheumatology, ISSN 0770-3198, 2009, Volume 28, Issue 8, pp. 975 - 978
Familial Mediterranean fever (FMF) is the most common inherited periodic fever syndrome characterized by recurrent episodes of serositis. Recently, a few...
Mean platelet volume | Familial Mediterranean fever | Children | Atherosclerosis | INTIMA-MEDIA THICKNESS | ACTIVATION | COLCHICINE | MARKERS | RHEUMATOLOGY | INTERLEUKIN-6 | Severity of Illness Index | Colchicine - therapeutic use | Humans | Male | Blood Platelets - physiology | Familial Mediterranean Fever - drug therapy | Case-Control Studies | Tubulin Modulators - therapeutic use | Familial Mediterranean Fever - blood | Platelet Count | Platelet Activation | Female | C-Reactive Protein - analysis | Child | Genetic aspects | Medical examination | Colchicine | Blood | Drug therapy
Mean platelet volume | Familial Mediterranean fever | Children | Atherosclerosis | INTIMA-MEDIA THICKNESS | ACTIVATION | COLCHICINE | MARKERS | RHEUMATOLOGY | INTERLEUKIN-6 | Severity of Illness Index | Colchicine - therapeutic use | Humans | Male | Blood Platelets - physiology | Familial Mediterranean Fever - drug therapy | Case-Control Studies | Tubulin Modulators - therapeutic use | Familial Mediterranean Fever - blood | Platelet Count | Platelet Activation | Female | C-Reactive Protein - analysis | Child | Genetic aspects | Medical examination | Colchicine | Blood | Drug therapy
Journal Article
Rheumatology International, ISSN 0172-8172, 9/2014, Volume 34, Issue 9, pp. 1323 - 1327
Henoch–Schönlein purpura (HSP) is the most common systemic vasculitis of childhood. Gastrointestinal (GI) bleeding is one of the major complications of HSP....
Medicine & Public Health | Neutrophil-to-lymphocyte ratio | Gastrointestinal bleeding | Rheumatology | Henoch–Schönlein purpura | Henoch-Schönlein purpura | Henoch-Schonlein purpura | OUTCOMES | RHEUMATOLOGY | ASSOCIATION | CHILDHOOD | CHILDREN | Lymphocyte Count | Mean Platelet Volume | Leukocyte Count | Purpura, Schoenlein-Henoch - physiopathology | Humans | Purpura (Pathology) | Hemoglobin | Heat shock proteins | Lymphocytes | Analysis
Medicine & Public Health | Neutrophil-to-lymphocyte ratio | Gastrointestinal bleeding | Rheumatology | Henoch–Schönlein purpura | Henoch-Schönlein purpura | Henoch-Schonlein purpura | OUTCOMES | RHEUMATOLOGY | ASSOCIATION | CHILDHOOD | CHILDREN | Lymphocyte Count | Mean Platelet Volume | Leukocyte Count | Purpura, Schoenlein-Henoch - physiopathology | Humans | Purpura (Pathology) | Hemoglobin | Heat shock proteins | Lymphocytes | Analysis
Journal Article
Turkish Journal of Pediatrics, ISSN 0041-4301, 2017, Volume 59, Issue 4, pp. 357 - 368
Pediatric patients with autoinflammatory or rheumatic diseases are at increased risk of infections; therefore, safe and effective immunizations are crucial in...
Live-atenuated vaccine | Pediatric rheumatic disease | Vaccination | Biologicals | SYSTEMIC-LUPUS-ERYTHEMATOSUS | ANTI-TNF | IMMUNIZATION PRACTICES ACIP | JUVENILE IDIOPATHIC ARTHRITIS | pediatric rheumatic disease | biologicals | ADVISORY-COMMITTEE | INFLAMMATORY-BOWEL-DISEASE | PNEUMOCOCCAL POLYSACCHARIDE VACCINE | HEPATITIS-B VACCINATION | IMMUNE-RESPONSES | PEDIATRICS | live-atenuated vaccine | CLINICAL-PRACTICE | vaccination | Immunocompromised Host - immunology | Rheumatic Diseases - drug therapy | Vaccination - methods | Humans | Immunosuppressive Agents - therapeutic use | Immunosuppressive Agents - adverse effects | Vaccination - adverse effects | Child | Practice Guidelines as Topic | Rheumatic Diseases - immunology
Live-atenuated vaccine | Pediatric rheumatic disease | Vaccination | Biologicals | SYSTEMIC-LUPUS-ERYTHEMATOSUS | ANTI-TNF | IMMUNIZATION PRACTICES ACIP | JUVENILE IDIOPATHIC ARTHRITIS | pediatric rheumatic disease | biologicals | ADVISORY-COMMITTEE | INFLAMMATORY-BOWEL-DISEASE | PNEUMOCOCCAL POLYSACCHARIDE VACCINE | HEPATITIS-B VACCINATION | IMMUNE-RESPONSES | PEDIATRICS | live-atenuated vaccine | CLINICAL-PRACTICE | vaccination | Immunocompromised Host - immunology | Rheumatic Diseases - drug therapy | Vaccination - methods | Humans | Immunosuppressive Agents - therapeutic use | Immunosuppressive Agents - adverse effects | Vaccination - adverse effects | Child | Practice Guidelines as Topic | Rheumatic Diseases - immunology
Journal Article
Clinical Rheumatology, ISSN 0770-3198, 5/2016, Volume 35, Issue 5, pp. 1237 - 1244
Familial Mediterranean fever (FMF) is the most common inherited autoinflammatory disease in the world. The long-term effects of subclinical inflammation in FMF...
Head upright tilt test | Familial Mediterranean fever | Medicine & Public Health | Autonomic Function | Rheumatology | RHEUMATOID-ARTHRITIS | DIAGNOSIS | SYSTEMIC-LUPUS-ERYTHEMATOSUS | RHEUMATOLOGY | IMPAIRMENT | COLCHICINE | FIBROMYALGIA | AMYLOIDOSIS | QT DISPERSION | DYSFUNCTION | PITUITARY-ADRENAL AXIS | Heart - physiopathology | Cross-Sectional Studies | Humans | Familial Mediterranean Fever - complications | Male | Primary Dysautonomias - physiopathology | Autonomic Nervous System - physiopathology | Primary Dysautonomias - complications | Familial Mediterranean Fever - physiopathology | Adolescent | Electrocardiography | Heart Rate - physiology | Female | Blood Pressure - physiology | Child | Electrocardiography, Ambulatory | Genetic aspects | Heart beat | Electrocardiogram
Head upright tilt test | Familial Mediterranean fever | Medicine & Public Health | Autonomic Function | Rheumatology | RHEUMATOID-ARTHRITIS | DIAGNOSIS | SYSTEMIC-LUPUS-ERYTHEMATOSUS | RHEUMATOLOGY | IMPAIRMENT | COLCHICINE | FIBROMYALGIA | AMYLOIDOSIS | QT DISPERSION | DYSFUNCTION | PITUITARY-ADRENAL AXIS | Heart - physiopathology | Cross-Sectional Studies | Humans | Familial Mediterranean Fever - complications | Male | Primary Dysautonomias - physiopathology | Autonomic Nervous System - physiopathology | Primary Dysautonomias - complications | Familial Mediterranean Fever - physiopathology | Adolescent | Electrocardiography | Heart Rate - physiology | Female | Blood Pressure - physiology | Child | Electrocardiography, Ambulatory | Genetic aspects | Heart beat | Electrocardiogram
Journal Article
Rheumatology International, ISSN 0172-8172, 9/2014, Volume 34, Issue 9, pp. 1337 - 1337
Journal Article
Arthritis & Rheumatology, ISSN 2326-5191, 10/2014, Volume 66, Issue 10, pp. 2871 - 2880
Objective To compare the capacity of the 2004 diagnostic guidelines for hemophagocytic lymphohistiocytosis (HLH‐2004) with the capacity of the preliminary...
DISEASE | INDICATOR | DISORDERS | RATIO | AGREEMENT | RHEUMATOLOGY | HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS | CHILDREN | Macrophage Activation Syndrome - diagnosis | Diagnosis, Differential | Humans | Child, Preschool | Lymphohistiocytosis, Hemophagocytic - diagnosis | Infant | Macrophage Activation Syndrome - complications | Male | Arthritis, Juvenile - complications | Female | Retrospective Studies | In Vitro Techniques | Child | Practice Guidelines as Topic
DISEASE | INDICATOR | DISORDERS | RATIO | AGREEMENT | RHEUMATOLOGY | HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS | CHILDREN | Macrophage Activation Syndrome - diagnosis | Diagnosis, Differential | Humans | Child, Preschool | Lymphohistiocytosis, Hemophagocytic - diagnosis | Infant | Macrophage Activation Syndrome - complications | Male | Arthritis, Juvenile - complications | Female | Retrospective Studies | In Vitro Techniques | Child | Practice Guidelines as Topic
Journal Article
Rheumatology International, ISSN 0172-8172, 9/2014, Volume 34, Issue 9, pp. 1333 - 1333
Journal Article
Anti-Inflammatory and Anti-Allergy Agents in Medicinal Chemistry, ISSN 1871-5230, 03/2010, Volume 9, Issue 1, pp. 41 - 45
Juvenile Idiopathic Arthritis (JIA) is an 'umbrella' term which is used to cover Juvenile Rheumatoid Arthritis (JRA) and Juvenile Chronic Arthritis (JCA)....
Treatment | Biologic agents | Juvenile idiopathic arthritis
Treatment | Biologic agents | Juvenile idiopathic arthritis
Journal Article
Clinical Rheumatology, ISSN 0770-3198, 4/2010, Volume 29, Issue 4, pp. 375 - 379
Familial Mediterranean fever (FMF) is the most common autoinflammatory disease which requires a lifelong treatment. The aim of this study was to evaluate the...
Medicine & Public Health | Rheumatology | Depression | Anxiety | Familial Mediterranean fever | Children | Adolescents | COLCHICINE | AMYLOIDOSIS | RISK | QUALITY-OF-LIFE | HEALTH | EPILEPSY | RHEUMATOLOGY | Depression - etiology | Humans | Adolescent | Familial Mediterranean Fever - psychology | Familial Mediterranean Fever - complications | Female | Male | Child | Anxiety - etiology | Case-Control Studies | Psychological aspects | Depression, Mental | Genetic aspects | Child psychopathology
Medicine & Public Health | Rheumatology | Depression | Anxiety | Familial Mediterranean fever | Children | Adolescents | COLCHICINE | AMYLOIDOSIS | RISK | QUALITY-OF-LIFE | HEALTH | EPILEPSY | RHEUMATOLOGY | Depression - etiology | Humans | Adolescent | Familial Mediterranean Fever - psychology | Familial Mediterranean Fever - complications | Female | Male | Child | Anxiety - etiology | Case-Control Studies | Psychological aspects | Depression, Mental | Genetic aspects | Child psychopathology
Journal Article
10.
Evaluation of restless legs syndrome and growing pains in children with familial mediterranean fever
Turkish Journal of Pediatrics, ISSN 0041-4301, 2018, Volume 60, Issue 2, pp. 159 - 164
Growing pains (GP) and restless leg syndrome (RLS) are one of the frequently seen pain syndromes of childhood. These two pain syndromes -GP and RLS-may be...
Restless legs syndrome | Exertional leg pain | Growing pains | Familial mediterranean fever | CRITERIA | DIAGNOSIS | DISEASES | growing pains | restless legs syndrome | PEDIATRICS | familial Mediterranean fever
Restless legs syndrome | Exertional leg pain | Growing pains | Familial mediterranean fever | CRITERIA | DIAGNOSIS | DISEASES | growing pains | restless legs syndrome | PEDIATRICS | familial Mediterranean fever
Journal Article
Annals of the Rheumatic Diseases, ISSN 0003-4967, 12/2012, Volume 71, Issue 12, pp. 1991 - 1997
Objectives Juvenile idiopathic arthritis (JIA) is a chronic inflammatory joint disease affecting children. Even if remission is successfully induced, about...
CLINICAL REMISSION | RHEUMATOID-ARTHRITIS | CRITERIA | NEUTROPHIL ACTIVATION | DISEASE | SELECT CATEGORIES | RHEUMATOLOGY | Biomarkers - metabolism | Recurrence | Calgranulin B - metabolism | Calgranulin A - metabolism | Humans | Leukocyte L1 Antigen Complex - metabolism | Risk Factors | Kaplan-Meier Estimate | Male | S100 Proteins - metabolism | Drug Monitoring - methods | Phagocytes - metabolism | Remission Induction | Arthritis, Juvenile - drug therapy | Arthritis, Juvenile - metabolism | S100A12 Protein | C-Reactive Protein - metabolism | Sensitivity and Specificity | ATP-Binding Cassette Transporters - metabolism | Female | Arthritis, Juvenile - epidemiology | Child | Antirheumatic Agents - therapeutic use | Control | Care and treatment | C-reactive protein | Juvenile arthritis | Physiological aspects | Inflammation | Research | Diagnosis | Biological markers | Health aspects | Immune system | Proteins | Immunology | Statistical analysis | Cytokines | Granulocytes | Laboratories | Bowel disease | Neutrophils | Biomarkers | Arthritis | Patients
CLINICAL REMISSION | RHEUMATOID-ARTHRITIS | CRITERIA | NEUTROPHIL ACTIVATION | DISEASE | SELECT CATEGORIES | RHEUMATOLOGY | Biomarkers - metabolism | Recurrence | Calgranulin B - metabolism | Calgranulin A - metabolism | Humans | Leukocyte L1 Antigen Complex - metabolism | Risk Factors | Kaplan-Meier Estimate | Male | S100 Proteins - metabolism | Drug Monitoring - methods | Phagocytes - metabolism | Remission Induction | Arthritis, Juvenile - drug therapy | Arthritis, Juvenile - metabolism | S100A12 Protein | C-Reactive Protein - metabolism | Sensitivity and Specificity | ATP-Binding Cassette Transporters - metabolism | Female | Arthritis, Juvenile - epidemiology | Child | Antirheumatic Agents - therapeutic use | Control | Care and treatment | C-reactive protein | Juvenile arthritis | Physiological aspects | Inflammation | Research | Diagnosis | Biological markers | Health aspects | Immune system | Proteins | Immunology | Statistical analysis | Cytokines | Granulocytes | Laboratories | Bowel disease | Neutrophils | Biomarkers | Arthritis | Patients
Journal Article
Annals of the Rheumatic Diseases, ISSN 0003-4967, 10/2019, Volume 78, Issue 10, pp. 1357 - 1362
ObjectiveTo develop and validate a diagnostic score that aids in identifying macrophage activation syndrome (MAS) in patients with systemic juvenile idiopathic...
GUIDELINES | RHEUMATOLOGY | FEATURES
GUIDELINES | RHEUMATOLOGY | FEATURES
Journal Article
Annals of the Rheumatic Diseases, ISSN 0003-4967, 12/2018, Volume 77, Issue 12, pp. 1710 - 1719
ObjectivesTo evaluate the long-term efficacy and safety of canakinumab in patients with active systemic juvenile idiopathic arthritis (JIA).MethodsPatients...
clinical trial | systemic juvenile idiopathic arthritis | canakinumab | long-term extension | interleukin-1β | CRITERIA | EFFICACY | SAFETY | MACROPHAGE ACTIVATION SYNDROME | DOUBLE-BLIND | PRELIMINARY DEFINITION | PLACEBO-CONTROLLED TRIAL | SELECT CATEGORIES | RHEUMATOLOGY | DISEASE-ACTIVITY | CHILDREN | Pediatrics | Glucocorticoids | Pathogenesis | Rheumatology | Clinical trials | Arthritis | Macrophages | Patients | Cell activation | Collaboration | Questionnaires | Rheumatism | TNF inhibitors | Remission | Safety | Drug dosages | Clinical and Epidemiological Research | 2311 | 1506
clinical trial | systemic juvenile idiopathic arthritis | canakinumab | long-term extension | interleukin-1β | CRITERIA | EFFICACY | SAFETY | MACROPHAGE ACTIVATION SYNDROME | DOUBLE-BLIND | PRELIMINARY DEFINITION | PLACEBO-CONTROLLED TRIAL | SELECT CATEGORIES | RHEUMATOLOGY | DISEASE-ACTIVITY | CHILDREN | Pediatrics | Glucocorticoids | Pathogenesis | Rheumatology | Clinical trials | Arthritis | Macrophages | Patients | Cell activation | Collaboration | Questionnaires | Rheumatism | TNF inhibitors | Remission | Safety | Drug dosages | Clinical and Epidemiological Research | 2311 | 1506
Journal Article
Clinical Rheumatology, ISSN 0770-3198, 12/2009, Volume 28, Issue 12, pp. 1389 - 1393
Familial Mediterranean fever (FMF) is the most common inherited autoinflammatory disease, which is caused by an inborn error in innate immune system. It was...
Disease severity | Breast-feeding | Innate immunity | Familial Mediterranean fever | PROTECTION | GUT | CHILDHOOD LEUKEMIA | RHEUMATOLOGY | MEFV-GENE | CHILDREN | HUMAN-MILK | RISK-FACTOR | AMYLOIDOSIS | DISEASE | Severity of Illness Index | Cytoskeletal Proteins - genetics | Humans | Breast Feeding | Familial Mediterranean Fever - genetics | Child, Preschool | Familial Mediterranean Fever - complications | Male | Pyrin | Young Adult | Erythema - etiology | Familial Mediterranean Fever - physiopathology | Time Factors | DNA Mutational Analysis | Adolescent | Arthritis - etiology | Female | Surveys and Questionnaires | Amyloidosis - etiology | Mutation | Child | Genetic aspects | Breast feeding | Cattle | Medical research | Breastfeeding & lactation | Immune system
Disease severity | Breast-feeding | Innate immunity | Familial Mediterranean fever | PROTECTION | GUT | CHILDHOOD LEUKEMIA | RHEUMATOLOGY | MEFV-GENE | CHILDREN | HUMAN-MILK | RISK-FACTOR | AMYLOIDOSIS | DISEASE | Severity of Illness Index | Cytoskeletal Proteins - genetics | Humans | Breast Feeding | Familial Mediterranean Fever - genetics | Child, Preschool | Familial Mediterranean Fever - complications | Male | Pyrin | Young Adult | Erythema - etiology | Familial Mediterranean Fever - physiopathology | Time Factors | DNA Mutational Analysis | Adolescent | Arthritis - etiology | Female | Surveys and Questionnaires | Amyloidosis - etiology | Mutation | Child | Genetic aspects | Breast feeding | Cattle | Medical research | Breastfeeding & lactation | Immune system
Journal Article
Annals of the Rheumatic Diseases, ISSN 0003-4967, 05/2010, Volume 69, Issue 5, pp. 790 - 797
Objectives To report methodology and overall clinical, laboratory and radiographic characteristics for Henoch–Schönlein purpura (HSP), childhood polyarteritis...
JUVENILE DERMATOMYOSITIS | SYSTEMIC-LUPUS-ERYTHEMATOSUS | PROSPECTIVE VALIDATION | COLLEGE | INTERNATIONAL CONSENSUS | PRELIMINARY DEFINITION | CLASSIFICATION | RHEUMATOLOGY | RHEUMATOLOGY 1990 CRITERIA | ACTIVITY CORE SET | DISEASE-ACTIVITY | Granulomatosis with Polyangiitis - diagnosis | Polyarteritis Nodosa - diagnosis | Takayasu Arteritis - diagnosis | Reproducibility of Results | Humans | International Cooperation | Purpura, Schoenlein-Henoch - diagnosis | Purpura, Schoenlein-Henoch - classification | Takayasu Arteritis - classification | Delphi Technique | Biopsy | Adolescent | Granulomatosis with Polyangiitis - classification | Internet | Polyarteritis Nodosa - classification | Child | Studies | Datasets | Nephrology | Kawasaki disease | Working groups | Physicians | Laboratories | Classification | Rheumatology | Data collection | Adults | Agreements
JUVENILE DERMATOMYOSITIS | SYSTEMIC-LUPUS-ERYTHEMATOSUS | PROSPECTIVE VALIDATION | COLLEGE | INTERNATIONAL CONSENSUS | PRELIMINARY DEFINITION | CLASSIFICATION | RHEUMATOLOGY | RHEUMATOLOGY 1990 CRITERIA | ACTIVITY CORE SET | DISEASE-ACTIVITY | Granulomatosis with Polyangiitis - diagnosis | Polyarteritis Nodosa - diagnosis | Takayasu Arteritis - diagnosis | Reproducibility of Results | Humans | International Cooperation | Purpura, Schoenlein-Henoch - diagnosis | Purpura, Schoenlein-Henoch - classification | Takayasu Arteritis - classification | Delphi Technique | Biopsy | Adolescent | Granulomatosis with Polyangiitis - classification | Internet | Polyarteritis Nodosa - classification | Child | Studies | Datasets | Nephrology | Kawasaki disease | Working groups | Physicians | Laboratories | Classification | Rheumatology | Data collection | Adults | Agreements
Journal Article
Clinical rheumatology, ISSN 0770-3198, 03/2019, Volume 38, Issue 3, pp. 645 - 645
The name of the last author of this article was incorrectly presented as "Cogulu Ozgur" this should have been "Ozgur Cogulu".
Medicine, Experimental | Medical research | Genetic aspects | MicroRNA | Analysis | Medical genetics | Familial Mediterranean fever
Medicine, Experimental | Medical research | Genetic aspects | MicroRNA | Analysis | Medical genetics | Familial Mediterranean fever
Journal Article
17.
Paediatric Behçet's disease with sinus venous thrombosis: experience from three centres from Turkey
Clinical and experimental rheumatology, ISSN 0392-856X, 07/2019
To report our experiences of the juvenile Behçet's disease (BD) patients with cerebral venous sinus thrombosis (CVST) and to review previous studies reporting...
Journal Article
Clinical Rheumatology, ISSN 0770-3198, 2009, Volume 28, Issue 10, pp. 1225 - 1228
Henoch-Schonlein purpura (HSP) is the most common systemic vasculitis in children. Gastrointestinal (GI) bleeding is one of the major complications affecting...
Mean platelet volume | Henoch-Schönlein purpura | Gastrointestinal bleeding | CRITERIA | MARKER | CLASSIFICATION | Henoch-Schonlein purpura | RHEUMATOLOGY | INTERLEUKIN-6 | THROMBOPOIETIN | CHILDHOOD | CHILDREN | INFLAMMATORY-BOWEL-DISEASE | THROMBOCYTOSIS | Predictive Value of Tests | Humans | Risk Factors | Child, Preschool | Male | Gastrointestinal Hemorrhage - epidemiology | Case-Control Studies | C-Reactive Protein - metabolism | Platelet Count | Purpura, Schoenlein-Henoch - complications | Female | Purpura, Schoenlein-Henoch - blood | Leukocyte Count | Retrospective Studies | Child | Purpura (Pathology) | Heat shock proteins | Medical research
Mean platelet volume | Henoch-Schönlein purpura | Gastrointestinal bleeding | CRITERIA | MARKER | CLASSIFICATION | Henoch-Schonlein purpura | RHEUMATOLOGY | INTERLEUKIN-6 | THROMBOPOIETIN | CHILDHOOD | CHILDREN | INFLAMMATORY-BOWEL-DISEASE | THROMBOCYTOSIS | Predictive Value of Tests | Humans | Risk Factors | Child, Preschool | Male | Gastrointestinal Hemorrhage - epidemiology | Case-Control Studies | C-Reactive Protein - metabolism | Platelet Count | Purpura, Schoenlein-Henoch - complications | Female | Purpura, Schoenlein-Henoch - blood | Leukocyte Count | Retrospective Studies | Child | Purpura (Pathology) | Heat shock proteins | Medical research
Journal Article