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Science, ISSN 0036-8075, 7/2012, Volume 337, Issue 6090, pp. 96 - 100
Pyruvate constitutes a critical branch point in cellular carbon metabolism. We have identified two proteins, Mpc1 and Mpc2, as essential for mitochondrial... 
Yeasts | Mitochondria | Diet | Plasmids | Drosophila | REPORTS | Amino acids | Oxidation | Respiration | Sugars | Medical schools | RAT-LIVER | TRANSPORT | COMPLEX | MECHANISM | IDENTIFICATION | MULTIDISCIPLINARY SCIENCES | Metabolomics | Humans | Molecular Sequence Data | Mitochondrial Proteins - genetics | Drosophila Proteins - metabolism | Drosophila melanogaster - genetics | Anion Transport Proteins - chemistry | Mitochondrial Membrane Transport Proteins - genetics | Drosophila melanogaster - metabolism | Saccharomyces cerevisiae - metabolism | Amino Acids - metabolism | Biological Transport | Mitochondrial Proteins - metabolism | Pyruvic Acid - metabolism | Amino Acid Sequence | Mitochondrial Membrane Transport Proteins - chemistry | Mitochondrial Membrane Transport Proteins - metabolism | Oxidation-Reduction | Carbohydrate Metabolism | Mitochondria - metabolism | Drosophila Proteins - chemistry | Saccharomyces cerevisiae Proteins - genetics | Anion Transport Proteins - metabolism | Citric Acid Cycle | Mitochondrial Membranes - metabolism | Point Mutation | Animals | Drosophila melanogaster - chemistry | Mitochondrial Proteins - chemistry | Saccharomyces cerevisiae Proteins - metabolism | Drosophila Proteins - genetics | Anion Transport Proteins - genetics | Saccharomyces cerevisiae Proteins - chemistry | Cell metabolism | Pyruvates | Chemical properties | Research | Molecular biology | Proteins | Yeast | Metabolism | Carriers | Human | Bacteria | Transport | Transporter
Journal Article
Journal Article
Journal Article
Journal Article
Molecular and Cellular Biology, ISSN 0270-7306, 04/2005, Volume 25, Issue 8, pp. 3286 - 3294
Article Usage Stats Services MCB Citing Articles Google Scholar PubMed Related Content Social Bookmarking CiteULike Delicious Digg Facebook Google+ Mendeley... 
SPINAL MUSCULAR-ATROPHY | RECOGNITION | BIOCHEMISTRY & MOLECULAR BIOLOGY | FRONTOTEMPORAL DEMENTIA | COMPLEX DEFICIENCY | GENE-EXPRESSION | ENHANCER | SMN2 | TAU | EXONIC MUTATIONS | MISSENSE MUTATIONS | CELL BIOLOGY | Gene Expression
Journal Article
Orphanet journal of rare diseases, ISSN 1750-1172, 2010, Volume 5, Issue 1, pp. 26 - 26
Journal Article
Human mutation, ISSN 1059-7794, 2010, Volume 31, Issue 7, pp. E1564 - E1573
Journal Article
Circulation, ISSN 0009-7322, 11/1999, Volume 100, Issue 22, pp. 2248 - 2253
Background-The clinical manifestations of inherited disorders of fatty acid oxidation vary according to the enzymatic defect. They may present as isolated... 
Arrhythmia | Metabolism | Fatty acids | CARNITINE | CARDIAC & CARDIOVASCULAR SYSTEMS | fatty acids | SUDDEN-DEATH | LONG-CHAIN | INBORN-ERRORS | HEART | ACYLCARNITINE TRANSLOCASE DEFICIENCY | CARDIOMYOPATHIES | arrhythmia | PERIPHERAL VASCULAR DISEASE | metabolism | PERHEXILINE | HEMATOLOGY | CULTURED FIBROBLASTS
Journal Article
Journal of Inherited Metabolic Disease, ISSN 1573-2665, 12/2010, Volume 33, Issue S3, pp. 443 - 453
Journal Article