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American journal of respiratory and critical care medicine, ISSN 1535-4970, 2014, Volume 190, Issue 2, pp. 175 - 184
Rationale: Ivacaftor is a cystic fibrosis transmembrane conductance regulator (CFTR) potentiator recently approved for patients with CF age 6 and older with... 
Cystic fibrosis | Pseudomonas aeruginosa | Ivacaftor | CFTR modulator | LUNG-FUNCTION | ivacaftor | MUCIN SECRETION | ADRENERGIC SWEAT SECRETION | MUCOCILIARY CLEARANCE | INTESTINAL PH | CHILDREN | RESPIRATORY SYSTEM | cystic fibrosis | PSEUDOMONAS-AERUGINOSA | INFLAMMATION | DISEASE | QUESTIONNAIRE | CRITICAL CARE MEDICINE | Sputum - microbiology | Lung - microbiology | Pseudomonas aeruginosa - isolation & purification | Follow-Up Studies | Forced Expiratory Volume - drug effects | Sweat - drug effects | Humans | Microbiota - drug effects | Respiratory System Agents - therapeutic use | Hospitalization - statistics & numerical data | Male | Aminophenols - therapeutic use | Quinolones - pharmacology | Aminophenols - pharmacology | Mucociliary Clearance - drug effects | Pseudomonas Infections - prevention & control | Young Adult | Hydrogen-Ion Concentration - drug effects | Quinolones - therapeutic use | Adult | Female | Lung - metabolism | Child | Biomarkers - metabolism | Respiratory System Agents - pharmacology | Cystic Fibrosis - metabolism | Cystic Fibrosis - microbiology | Pseudomonas Infections - complications | Pseudomonas Infections - diagnosis | Treatment Outcome | Lung - physiopathology | Genetic Markers | Sputum - metabolism | Cystic Fibrosis - genetics | Intestine, Small - drug effects | Lung - drug effects | Adolescent | Cystic Fibrosis Transmembrane Conductance Regulator - genetics | Intestine, Small - metabolism | Mutation | Cystic Fibrosis - drug therapy | Sweat - metabolism | Original
Journal Article
Journal Article
Digestive diseases and sciences, ISSN 1573-2568, 2015, Volume 61, Issue 1, pp. 198 - 207
... After Treatment with Ivacaftor Drucy Borowitz 1 • Barry Lubarsky 2 • Michael Wilschanski 3 • Anne Munck 4 • Daniel Gelfond 5 • Frank Bodewes 6 • Sarah Jane Schwarzenberg 7... 
Growth | FECAL ELASTASE-1 | Kalydeco | CFTR POTENTIATOR | Weight gain | CHILDREN | TRANSMEMBRANE CONDUCTANCE REGULATOR | Bicarbonate | FAT MALABSORPTION | ENERGY-EXPENDITURE | THERAPY | Potentiator | DISEASE | QUALITY-OF-LIFE | Cystic fibrosis transmembrane conductance regulator | BICARBONATE SECRETION | Biochemistry, general | Medicine & Public Health | Hepatology | Gastroenterology | Oncology | Transplant Surgery | GASTROENTEROLOGY & HEPATOLOGY | Cystic Fibrosis - physiopathology | Humans | Male | Young Adult | Time Factors | Adult | Female | Surveys and Questionnaires | Weight Gain - drug effects | Child | Genetic Predisposition to Disease | Double-Blind Method | Drug Administration Schedule | Administration, Oral | Cystic Fibrosis - metabolism | Cystic Fibrosis Transmembrane Conductance Regulator - agonists | Treatment Outcome | Cystic Fibrosis Transmembrane Conductance Regulator - metabolism | Membrane Transport Modulators - administration & dosage | Phenotype | Quinolones - administration & dosage | Cystic Fibrosis - genetics | Nutritional Status - drug effects | Adolescent | Cystic Fibrosis - diagnosis | Cystic Fibrosis Transmembrane Conductance Regulator - genetics | Mutation | Aminophenols - administration & dosage | Cystic Fibrosis - drug therapy | Cystic fibrosis | Care and treatment | Genetic aspects | Carbonates | Body image | Analysis
Journal Article
Pediatric Clinics of North America, ISSN 0031-3955, 08/2016, Volume 63, Issue 4, pp. xvii - xviii
...Susan G. Marshall, MD, Editor Drucy Borowitz, MD, Editor Living with Cystic Fibrosis (CF) is a challenge, but advances in medical care for people with CF... 
Journal Article