X
Search Filters
Format Format
Subjects Subjects
Subjects Subjects
X
Sort by Item Count (A-Z)
Filter by Count
index medicus (19) 19
coenzyme q (18) 18
biochemistry & molecular biology (16) 16
cell biology (16) 16
ubiquinone (16) 16
mitochondria (14) 14
mutation (13) 13
saccharomyces-cerevisiae (13) 13
humans (12) 12
oxidative stress (12) 12
ubiquinone - genetics (12) 12
ubiquinone - metabolism (12) 12
yeast (11) 11
biosynthesis (10) 10
ubiquinone biosynthesis (10) 10
biophysics (9) 9
saccharomyces cerevisiae - genetics (9) 9
saccharomyces cerevisiae - metabolism (8) 8
electron transport (7) 7
saccharomyces cerevisiae - enzymology (7) 7
ubiquinone - analogs & derivatives (7) 7
animals (6) 6
article (6) 6
cell membrane - metabolism (6) 6
cells (6) 6
enzymes (6) 6
gene (6) 6
mitochondria - enzymology (6) 6
mitochondria - metabolism (6) 6
oxidation-reduction (6) 6
phosphorylation (6) 6
respiration (6) 6
saccharomyces cerevisiae (6) 6
ubiquinone - biosynthesis (6) 6
antioxidants - metabolism (5) 5
ascorbic acid - metabolism (5) 5
cerebellar-ataxia (5) 5
child, preschool (5) 5
coenzyme q10 (5) 5
hela cells (5) 5
life sciences (5) 5
physiological aspects (5) 5
protein (5) 5
ubiquinone - deficiency (5) 5
bioenergetics (4) 4
caenorhabditis-elegans (4) 4
coenzymes (4) 4
expression (4) 4
geriatrics & gerontology (4) 4
life-span (4) 4
mitochondria - genetics (4) 4
mitochondrial proteins - genetics (4) 4
molecular biology (4) 4
nephrotic syndrome (4) 4
phosphatase (4) 4
plasma-membrane (4) 4
saccharomyces cerevisiae - growth & development (4) 4
saccharomyces cerevisiae proteins - metabolism (4) 4
ubiquinone - pharmacology (4) 4
ubiquinone - physiology (4) 4
ubiquinone deficiency (4) 4
amino acid sequence (3) 3
ascorbate stabilization (3) 3
ataxia (3) 3
ataxia - genetics (3) 3
coenzyme q deficiency (3) 3
coq deficiency (3) 3
cytochrome c (3) 3
fibroblasts (3) 3
fibroblasts - metabolism (3) 3
genes (3) 3
hl-60 cells (3) 3
kinase (3) 3
liver plasma-membrane (3) 3
membrane electron-transport (3) 3
metabolism (3) 3
mitochondria - pathology (3) 3
mitochondrial disease (3) 3
mitochondrial diseases (3) 3
mitochondrial diseases - genetics (3) 3
mitochondrial dna (3) 3
mitochondrial metabolism (3) 3
mitochondrial proteins - metabolism (3) 3
muscle biopsy (3) 3
muscle weakness - genetics (3) 3
mutations (3) 3
plasma membrane (3) 3
protein complex (3) 3
q biosynthesis (3) 3
rats (3) 3
redox system (3) 3
research (3) 3
research article (3) 3
steroid-resistant nephrotic syndrome (3) 3
ubiquinone - chemistry (3) 3
aging - drug effects (2) 2
alleles (2) 2
analysis (2) 2
antioxidants (2) 2
antioxidants - pharmacology (2) 2
more...
Language Language
Publication Date Publication Date
Click on a bar to filter by decade
Slide to change publication date range


BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR AND CELL BIOLOGY OF LIPIDS, ISSN 1388-1981, 11/2014, Volume 1841, Issue 11, pp. 1628 - 1638
Coq5 catalyzes the only C-methylation involved in the biosynthesis of coenzyme Q(Q or ubiquinone) in humans and yeast Saccharomyces cerevisiae. As one of... 
Q-biosynthetic intermediate | Protein complex | BIOCHEMISTRY & MOLECULAR BIOLOGY | MITOCHONDRIA | SACCHAROMYCES-CEREVISIAE | CELL BIOLOGY | YEAST | SUPPLEMENTATION | Mitochondrial metabolism | Human COQ gene | Ubiquinone | BIOPHYSICS | GENE | PARA-AMINOBENZOIC ACID | UBIQUINONE BIOSYNTHESIS | MUTATIONS | Saccharomyces cerevisiae | EXPRESSION | POLYPEPTIDE
Journal Article
Proceedings of the National Academy of Sciences of the United States of America, ISSN 0027-8424, 04/2017, Volume 114, Issue 15, pp. E3041 - E3050
Journal Article
BBA - Molecular and Cell Biology of Lipids, ISSN 1388-1981, 11/2014, Volume 1841, Issue 11, pp. 1628 - 1638
Coq5 catalyzes the only -methylation involved in the biosynthesis of coenzyme Q (Q or ubiquinone) in humans and yeast . As one of eleven polypeptides required... 
Q-biosynthetic intermediate | Mitochondrial metabolism | Protein complex | Human COQ gene | Ubiquinone | Saccharomyces cerevisiae
Journal Article
Proceedings of the National Academy of Sciences of the United States of America, ISSN 0027-8424, 04/2017, Volume 114, Issue 15, p. E3041
Regulation of mitochondrial activity allows cells to adapt to changing conditions and to control oxidative stress, and its dysfunction can lead to... 
Cytochrome | Tyrosine | Oxidative stress | Phosphorylation | Reactive oxygen species | Nuclear magnetic resonance--NMR | Phenylalanine | Heme proteins | Caspase | Cells | Cytochrome c | Mitochondria | Ischemia | Hypoxia | Peroxidase | Mutation | Cancer | Apoptosis
Journal Article
by Pañeda, A and Jiménez, I and Berlanga, A and Mork, A and Gaspar, B and Chuah, M K and Sgodda, M and Eggenschwiler, R and Möbus, S and Hoepfner, J and Kleinsorge, M and Papp, O and Sharma, A D and Broccoli, V and Broccoli, V and Tesar, P J and Dick, J E and De Luca, M and Birket, M and Meer, Bvan and Ribeiro, M and Passier, R and Bellin, M and Orlova, V and Davis, R and Freund, C and Kosmidis, G and Tertoolen, L and Giacca, M and Giacca, M and Goyenvalle, A and Leumann, C and Testa, G and Nehar, D and Courau, T and Qasim, W and Qasim, W and Sommermeyer, D and Liu, L and Maloney, D and Turtle, C and Maude, S L and Barrett, D M and Shaw, P A and Brogdon, J and Young, R and Marcucci, K T and Levine, B L and Frey, N and Porter, D L and Lacey, S F and Melenhorst, J J and Grupp, S A and Bonini, C and Friedmann-Morvinski, D and Soda, Y and Rommel, A and Myskiw, C and Kohn, D B and Wu, C and Espinoza, D A and Koelle, S J and Yang, D and Schlums, H and Kaur, A and Hammer, Q and Childs, R W and Romagnani, C and Bryceson, Y T and Scala, S and Scala, S and Scala, S and Pellin, D and Basso-Ricci, L and Basso-Ricci, L and Dionisio, F and Dionisio, F and Dionisio, F and Baricordi, C and Leonardelli, L and Leonardelli, L and Scaramuzza, S and Ferrua, F and Cicalese, M P and Giannelli, S and Giannelli, S and Neduva, V and Dow, D J and Roncarolo, M G and Ciceri, F and Ciceri, F and Vicard, P and Wit, E and Di Serio, C and Bonini, C and Naldini, L and Aiuti, A and Nelson, C E and Robinson-Hamm, J N and Bacchetta, Rosa and ...
Human Gene Therapy, ISSN 1043-0342, 11/2016, Volume 27, Issue 11, pp. A1 - A185
Journal Article
JOURNAL OF MEDICAL GENETICS, ISSN 0022-2593, 03/2012, Volume 49, Issue 3, pp. 187 - 191
Background COQ4 encodes a protein that organises the multienzyme complex for the synthesis of coenzyme Q(10) (CoQ(10)). A 3.9 Mb deletion of chromosome 9q34.13... 
YEAST | MITOCHONDRIAL ENCEPHALOMYOPATHY | GENE | BIOSYNTHESIS | GENETICS & HEREDITY | MUSCLE | COQ DEFICIENCY | MUTATIONS
Journal Article
Journal of Clinical Investigation, ISSN 0021-9738, 05/2011, Volume 121, Issue 5, pp. 2013 - 2024
Steroid-resistant nephrotic syndrome (SRNS) is a frequent cause of end-stage renal failure. Identification of single-gene causes of SRNS has generated some... 
MEDICINE, RESEARCH & EXPERIMENTAL | OXIDATIVE STRESS | GENE | COENZYME-Q BIOSYNTHESIS | DIPHOSPHATE SYNTHASE SUBUNIT-2 | NPHS2 | GLOMERULAR PROTEIN | UBIQUINONE BIOSYNTHESIS | COQ DEFICIENCY | FOCAL SEGMENTAL GLOMERULOSCLEROSIS | SACCHAROMYCES-CEREVISIAE | Deafness | Gene mutations | Genetic aspects | Nephrotic syndrome | Research | Health aspects | Risk factors
Journal Article
BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE, ISSN 0925-4439, 01/2014, Volume 1842, Issue 1, pp. 1 - 6
Human COQ6 encodes a monooxygenase which is responsible for the C5-hydroxylation of the quinone ring of coenzyme Q (CoQ). Mutations in COQ6 cause primary CoQ... 
Q BIOSYNTHESIS | BIOPHYSICS | SUBSTRATE | BIOCHEMISTRY & MOLECULAR BIOLOGY | Coenzyme Q | Vanillic acid | Steroid-resistant nephrotic syndrome | COQ6
Journal Article
EXPERT REVIEW OF MOLECULAR DIAGNOSTICS, ISSN 1473-7159, 08/2015, Volume 15, Issue 8, pp. 1049 - 1059
Coenzyme Q(10) (CoQ) deficiency syndromes comprise a growing number of neurological and extraneurological disorders. Primary-genetic but also secondary CoQ... 
next-generation sequencing | RESISTANT NEPHROTIC SYNDROME | MUSCLE | COQ DEFICIENCY | PATHOLOGY | muscle biopsy | SACCHAROMYCES-CEREVISIAE | coenzyme Q10 deficiency syndromes | mitochondrial diseases | MUTATIONS CAUSE | Q BIOSYNTHESIS | GENE | CEREBELLAR-ATAXIA | functional studies in yeasts | MITOCHONDRIAL DISORDERS | UBIQUINONE DEFICIENCY
Journal Article
BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS, ISSN 0005-2728, 11/2018, Volume 1859, Issue 11, pp. 1235 - 1248
Coenzyme Q(10) (CoQ(10)) is a redox molecule critical for the proper function of energy metabolism and antioxidant defenses. Despite its essential role in... 
Lipid synthesis | COMPLEX | ACID | METHYLTRANSFERASE | PHOSPHORYLATION | BIOCHEMISTRY & MOLECULAR BIOLOGY | KINASE | Coenzyme Q | Phosphatase | SACCHAROMYCES-CEREVISIAE | LIVE CELLS | YEAST | Mitochondria | PROTEIN PHOSPHATASES | BIOPHYSICS | Bioenergetics | EXPRESSION
Journal Article
EXPERT REVIEW OF MOLECULAR DIAGNOSTICS, ISSN 1473-7159, 2018, Volume 18, Issue 6, pp. 491 - 498
Introduction: Coenzyme Q(10) (CoQ) deficiency syndromes comprise a growing number of genetic disorders. While primary CoQ deficiency syndromes are rare... 
Coenzyme Q deficiency syndromes | OXIDATIVE STRESS | WHOLE-GENOME | SULFIDE OXIDATION | next generation sequencing | RENAL-DISEASE | PATHOLOGY | muscle biopsy | COQ BIOSYNTHESIS | oxidative phosphorylation | INBORN-ERRORS | mitochondrial diseases | CEREBELLAR-ATAXIA | MITOCHONDRIAL DYSFUNCTION | NEPHROTIC SYNDROME | UBIQUINONE DEFICIENCY
Journal Article
STEM CELL RESEARCH, ISSN 1873-5061, 10/2017, Volume 24, pp. 144 - 147
Wereport the generation, CRISPR/Cas9-edition and characterization of induced pluripotent stem cell (iPSC) lines froma patient with coenzyme Q(10) deficiency... 
PLURIPOTENT STEM-CELLS | BIOTECHNOLOGY & APPLIED MICROBIOLOGY | HUMAN B-CELLS | CELL & TISSUE ENGINEERING | CELL BIOLOGY
Journal Article
CELLULAR AND MOLECULAR LIFE SCIENCES, ISSN 1420-682X, 01/2009, Volume 66, Issue 1, pp. 173 - 186
Coenzyme Q is a lipid molecule required for respiration and antioxidant protection. Q biosynthesis in Saccharomyces cerevisiae requires nine proteins... 
MULTISUBUNIT COMPLEX | LIFE-SPAN | mitochondria | SIDE-CHAIN | BIOCHEMISTRY & MOLECULAR BIOLOGY | yeast regulation | SACCHAROMYCES-CEREVISIAE | CELL BIOLOGY | Ubiquinone | CAENORHABDITIS-ELEGANS | FUNCTIONAL EXPRESSION | ANTIOXIDANT SYSTEM | UBIQUINONE BIOSYNTHESIS | GENETIC-EVIDENCE | LIVED CLK-1 MUTANTS | coenzyme Q
Journal Article
Journal of Biological Chemistry, ISSN 0021-9258, 03/2002, Volume 277, Issue 13, pp. 10973 - 10981
Coenzyme Q (Q) is an essential component of the mitochondrial respiratory chain in eukaryotic cells but also is present in other cellular membranes where it... 
cytochrome bc1 | coq7 gene | succinate-cytochrome c | Coenzyme Q | succinic acid | cytochrome c
Journal Article
by Suma, Antonio and Micheletti, Cristian and Ludescher, Josef and Bunde, Armin and Schellnhuber, Hans Joachim and Wu, Grace C and Deshmukh, Ranjit and Ndhlukula, Kudakwashe and Radojicic, Tijana and Reilly-Moman, Jessica and Phadke, Amol and Kammen, Daniel M and Callaway, Duncan S and Morrison, Tiffany H and Vazao, Helena and Rosa, Susana and Barata, Tania and Costa, Ricardo and Pitrez, Patricia R and Honorio, Ines and de Vries, Margreet R and Papatsenko, Dimitri and Benedito, Rui and Saris, Daniel and Khademhosseini, Ali and Quax, Paul H. A and Pereira, Carlos F and Mercader, Nadia and Fernandes, Hugo and Ferreira, Lino and Henderson, Kate L and Felth, Lindsey C and Molzahn, Cristen M and Shkel, Irina and Wang, Si and Chhabra, Munish and Ruff, Emily F and Bieter, Lauren and Kraft, Joseph E and Record Jr., M. Thomas and Moreno-Beltran, Blas and Guerra-Castellano, Alejandra and Diaz-Quintana, Antonio and Del Conte, Rebecca and Garcia-Maurino, Sofia M and Diaz-Moreno, Sofia and Gonzalez-Arzola, Katiuska and Santos-Ocana, Carlos and Velazquez-Campoy, Adrian and De la Rosa, Miguel A and Turano, Paola and Diaz-Moreno, Irene and Lenaeus, Michael J and El-Din, Tamer M. Gamal and Ing, Christopher and Ramanadane, Karthik and Pomes, Regis and Zheng, Ning and Catterall, William A and Eser, Umut and Chandler-Brown, Devon and Ay, Ferhat and Straight, Aaron F and Duan, Zhijun and Noble, William Stafford and Skotheim, Jan M and Luo, Dan and de Morree, Antoine and Boutet, Stephane and Quach, Navaline and Natu, Vanita and Rustagi, Arjun and Rando, Thomas A and Ding, Yi and Ploper, Diego and Sosa, Eric A and Colozza, Gabriele and Moriyama, Yuki and Benitez, Maria D. J and Zhang, Kelvin and Merkurjev, Daria and De Robertis, Edward M and Braakman, Rogier and Follows, Michael J and Chisholm, Sallie W and Chawanthayatham, Supawadee and Valentine III, Charles C and Fedeles, Bogdan I and Fox, Edward J and Loeb, Lawrence A and Levine, Stuart S and Slocum, Stephen L and Wogan, Gerald N and Croy, Robert G and Essigmann, John M and Ali, Moustafa R. K and Rahman, Mohammad Aminur and Wu, Yue and Han, Tiegang and Peng, Xianghong and ...
Proceedings of the National Academy of Sciences of the United States, ISSN 0027-8424, 04/2017, Volume 114, Issue 15, pp. 3801 - 3804
Journal Article
BIOCHIMICA ET BIOPHYSICA ACTA-BIOMEMBRANES, ISSN 0005-2736, 06/2009, Volume 1788, Issue 6, pp. 1238 - 1248
Coenzyme Q is an isoprenylated benzoquinone lipid that functions in respiratory electron transport and as a lipid antioxidant. Dietary supplementation with Q... 
RAT-LIVER | LIFE-SPAN | BIOCHEMISTRY & MOLECULAR BIOLOGY | PREVACUOLAR COMPARTMENT | MITOCHONDRIAL-FUNCTION | Coenzyme Q | MEMBRANE ELECTRON-TRANSPORT | Mitochondrial disease | PLASMA-MEMBRANE | Endocytosis | Ubiquinone | CAENORHABDITIS-ELEGANS | BIOPHYSICS | Endomembrane | UBIQUINONE BIOSYNTHESIS | PROTONMOTIVE Q-CYCLE | Q uptake | PARKINSONS-DISEASE
Journal Article
Cellular and Molecular Life Sciences, ISSN 1420-682X, 01/2009, Volume 66, Issue 1, pp. 173 - 186
Journal Article
Cellular and Molecular Life Sciences, ISSN 1420-682X, 01/2009, Volume 66, Issue 1, pp. 173 - 186
Coenzyme Q is a lipid molecule required for respiration and antioxidant protection. Q biosynthesis in Saccharomyces cerevisiae requires nine proteins... 
Journal Article
No results were found for your search.

Cannot display more than 1000 results, please narrow the terms of your search.