2001, Seminars in liver disease, Volume 21, no. 4., ii, p. 469-595
Book
JAMA, ISSN 0098-7484, 05/2014, Volume 311, Issue 17, pp. 1750 - 1759
IMPORTANCE Biliary atresia is the most common cause of end-stage liver disease in children. Controversy exists as to whether use of steroids after...
IMPROVE | MEDICINE, GENERAL & INTERNAL | MANAGEMENT | ADJUVANT STEROID-THERAPY | KASAI PORTOENTEROSTOMY | OUTCOMES | FLOW | Prednisolone - adverse effects | Prednisolone - administration & dosage | Double-Blind Method | Administration, Oral | Humans | Infant | Male | Methylprednisolone - adverse effects | Treatment Outcome | Biliary Atresia - drug therapy | Adrenal Cortex Hormones - adverse effects | Bilirubin - blood | Portoenterostomy, Hepatic | Biliary Atresia - surgery | Survival Analysis | Drainage - methods | Female | Infusions, Intravenous | Adrenal Cortex Hormones - administration & dosage | Methylprednisolone - administration & dosage | Biliary atresia | Care and treatment | Corticosteroids | Surgery | Dosage and administration | Research | Health aspects | Liver diseases | Drug therapy | Medical treatment | Childrens health | Steroids
IMPROVE | MEDICINE, GENERAL & INTERNAL | MANAGEMENT | ADJUVANT STEROID-THERAPY | KASAI PORTOENTEROSTOMY | OUTCOMES | FLOW | Prednisolone - adverse effects | Prednisolone - administration & dosage | Double-Blind Method | Administration, Oral | Humans | Infant | Male | Methylprednisolone - adverse effects | Treatment Outcome | Biliary Atresia - drug therapy | Adrenal Cortex Hormones - adverse effects | Bilirubin - blood | Portoenterostomy, Hepatic | Biliary Atresia - surgery | Survival Analysis | Drainage - methods | Female | Infusions, Intravenous | Adrenal Cortex Hormones - administration & dosage | Methylprednisolone - administration & dosage | Biliary atresia | Care and treatment | Corticosteroids | Surgery | Dosage and administration | Research | Health aspects | Liver diseases | Drug therapy | Medical treatment | Childrens health | Steroids
Journal Article
Transplantation, ISSN 0041-1337, 07/2016, Volume 100, Issue 7, pp. 1440 - 1452
ABSTRACTTwo distinct pulmonary vascular disorders, hepatopulmonary syndrome (HPS) and portopulmonary hypertension (POPH) may occur as a consequence of hepatic...
SURGERY | SINGLE-CENTER EXPERIENCE | LONG-TERM RESPONSE | PULMONARY ARTERIAL-HYPERTENSION | LUNG PERFUSION SCAN | RANDOMIZED CONTROLLED-TRIAL | IMMUNOLOGY | CALCIUM-CHANNEL BLOCKERS | ARGININE METHYL-ESTER | TRANSPLANTATION | PORTOSYSTEMIC SHUNT TIPS | ENDOTHELIN-RECEPTOR ANTAGONIST | DISEASE MELD EXCEPTION | Hypertension, Pulmonary - diagnosis | Liver - pathology | Liver Transplantation | Prognosis | Gastroenterology - standards | Europe | Humans | Risk Factors | Hepatopulmonary Syndrome - surgery | Hypertension, Pulmonary - surgery | Male | Clinical Trials as Topic | Gastroenterology - methods | Societies, Medical | Female | Hepatopulmonary Syndrome - diagnosis | Liver - surgery | Research Design
SURGERY | SINGLE-CENTER EXPERIENCE | LONG-TERM RESPONSE | PULMONARY ARTERIAL-HYPERTENSION | LUNG PERFUSION SCAN | RANDOMIZED CONTROLLED-TRIAL | IMMUNOLOGY | CALCIUM-CHANNEL BLOCKERS | ARGININE METHYL-ESTER | TRANSPLANTATION | PORTOSYSTEMIC SHUNT TIPS | ENDOTHELIN-RECEPTOR ANTAGONIST | DISEASE MELD EXCEPTION | Hypertension, Pulmonary - diagnosis | Liver - pathology | Liver Transplantation | Prognosis | Gastroenterology - standards | Europe | Humans | Risk Factors | Hepatopulmonary Syndrome - surgery | Hypertension, Pulmonary - surgery | Male | Clinical Trials as Topic | Gastroenterology - methods | Societies, Medical | Female | Hepatopulmonary Syndrome - diagnosis | Liver - surgery | Research Design
Journal Article
Nature Reviews Gastroenterology and Hepatology, ISSN 1759-5045, 2019, Volume 16, Issue 6, pp. 346 - 360
Neonatal cholestasis is a group of rare disorders of impaired bile flow characterized by conjugated hyperbilirubinaemia in the newborn and young infant....
CONTROLLED-TRIAL | CHOLECYSTO-CHOLANGIOGRAPHY | LIVER-TRANSPLANTATION | URSODEOXYCHOLIC ACID | INTRAHEPATIC CHOLESTASIS | NUCLEAR RECEPTORS | PARENTERAL-NUTRITION | BILE-ACID SYNTHESIS | STOOL COLOR CARD | GASTROENTEROLOGY & HEPATOLOGY | BILIARY ATRESIA
CONTROLLED-TRIAL | CHOLECYSTO-CHOLANGIOGRAPHY | LIVER-TRANSPLANTATION | URSODEOXYCHOLIC ACID | INTRAHEPATIC CHOLESTASIS | NUCLEAR RECEPTORS | PARENTERAL-NUTRITION | BILE-ACID SYNTHESIS | STOOL COLOR CARD | GASTROENTEROLOGY & HEPATOLOGY | BILIARY ATRESIA
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Bone Density in Children With Chronic Liver Disease Correlates With Growth and Cholestasis
Hepatology, ISSN 0270-9139, 01/2019, Volume 69, Issue 1, pp. 245 - 257
Osteopenia and bone fractures are significant causes of morbidity in children with cholestatic liver disease. Dual‐energy X‐ray absorptiometry (DXA) analysis...
MINERAL DENSITY | MASS | SIZE | X-RAY ABSORPTIOMETRY | FRACTURES | MUTATIONS | GASTROENTEROLOGY & HEPATOLOGY | ASSOCIATION | LINEAGE | ALAGILLE SYNDROME | TRANSPLANTATION | Dual energy X-ray absorptiometry | Bile acids | Liver diseases | Alagille syndrome | Gallbladder diseases | Bilirubin | Morbidity | Bone mineral content | Body mass index | Fractures | Etiology | Bone mineral density | Bone density | Children | Osteopenia | Cholestasis | Population density | Bile
MINERAL DENSITY | MASS | SIZE | X-RAY ABSORPTIOMETRY | FRACTURES | MUTATIONS | GASTROENTEROLOGY & HEPATOLOGY | ASSOCIATION | LINEAGE | ALAGILLE SYNDROME | TRANSPLANTATION | Dual energy X-ray absorptiometry | Bile acids | Liver diseases | Alagille syndrome | Gallbladder diseases | Bilirubin | Morbidity | Bone mineral content | Body mass index | Fractures | Etiology | Bone mineral density | Bone density | Children | Osteopenia | Cholestasis | Population density | Bile
Journal Article
Journal of Pediatric Gastroenterology and Nutrition, ISSN 0277-2116, 09/2016, Volume 63, Issue 3, pp. 312 - 313
Journal Article
Journal of Pediatric Gastroenterology and Nutrition, ISSN 0277-2116, 09/2015, Volume 61, Issue 3, pp. 268 - 269
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Gastroenterology, ISSN 0016-5085, 05/2019, Volume 156, Issue 6, pp. S-1214 - S-1214
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Journal of Pediatric Gastroenterology and Nutrition, ISSN 0277-2116, 03/2016, Volume 62, Issue 3, pp. 360 - 362
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The Journal of Pediatrics, ISSN 0022-3476, 05/2018, Volume 196, pp. 14 - 21.e1
pulmonary vascular disease | chronic liver disease | cirrhosis | LIVER-TRANSPLANTATION | PULMONARY-HYPERTENSION | DISEASE | NITRIC-OXIDE | PEDIATRICS | COMPLICATIONS | ECHOCARDIOGRAPHY | OUTCOMES | CANDIDATES | PORTAL-HYPERTENSION | Hypertension, Pulmonary - diagnosis | Liver Cirrhosis - diagnosis | Prevalence | Liver Transplantation - adverse effects | Humans | Oximetry | Liver Cirrhosis - therapy | Hepatopulmonary Syndrome - therapy | Hypertension, Pulmonary - therapy | Hypertension, Portal - diagnosis | Mass Screening | Hypertension, Portal - therapy | Hepatopulmonary Syndrome - diagnosis | Child
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Hepatology, ISSN 0270-9139, 01/2019, Volume 69, Issue 1, pp. 245 - 257
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The Journal of pediatrics, ISSN 0022-3476, 11/2018, Volume 202, pp. 179 - 185.e4
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Journal of Pediatric Gastroenterology and Nutrition, ISSN 0277-2116, 04/2019, Volume 68, Issue 4, pp. 495 - 501
OBJECTIVES:Biliary atresia (BA) is a progressive neonatal fibroinflammatory cholangiopathy. We hypothesized that intravenous immunoglobulin (IVIg) would be...
Pediatric research | Biliary atresia | Care and treatment
Pediatric research | Biliary atresia | Care and treatment
Journal Article
Journal of Pediatric Gastroenterology and Nutrition, ISSN 0277-2116, 09/2019, p. 1
OBJECTIVES:To assess neurodevelopmental outcomes among children with biliary atresia (BA) surviving with their native liver at age 3–12 years and evaluate...
Journal Article
Gastroenterology, ISSN 0016-5085, 05/2018, Volume 154, Issue 6, pp. S-1092 - S-1092
Journal Article
Journal of Pediatric Gastroenterology and Nutrition, ISSN 0277-2116, 07/2015, Volume 61, Issue 1, pp. 94 - 101
OBJECTIVES:α-1-Antitrypsin (A1AT) deficiency is a common genetic disease with an unpredictable and highly variable course. The Childhood Liver Disease Research...
liver enzymes | metabolic liver disease | jaundice | liver transplant | cirrhosis | ALPHA-ANTITRYPSIN DEFICIENCY | ADULTS | DAMAGE | CHILDREN | MURINE MODEL | NUTRITION & DIETETICS | PEDIATRICS | GASTROENTEROLOGY & HEPATOLOGY | Liver - pathology | Prospective Studies | alpha 1-Antitrypsin - blood | Humans | Liver - metabolism | Child, Preschool | Infant | Male | Young Adult | alpha 1-Antitrypsin Deficiency - blood | Hypertension, Portal - etiology | alpha 1-Antitrypsin Deficiency - complications | Adolescent | Adult | Female | Hypertension, Portal - blood | Jaundice - epidemiology | Child | Longitudinal Studies | Infant, Newborn | Cohort Studies
liver enzymes | metabolic liver disease | jaundice | liver transplant | cirrhosis | ALPHA-ANTITRYPSIN DEFICIENCY | ADULTS | DAMAGE | CHILDREN | MURINE MODEL | NUTRITION & DIETETICS | PEDIATRICS | GASTROENTEROLOGY & HEPATOLOGY | Liver - pathology | Prospective Studies | alpha 1-Antitrypsin - blood | Humans | Liver - metabolism | Child, Preschool | Infant | Male | Young Adult | alpha 1-Antitrypsin Deficiency - blood | Hypertension, Portal - etiology | alpha 1-Antitrypsin Deficiency - complications | Adolescent | Adult | Female | Hypertension, Portal - blood | Jaundice - epidemiology | Child | Longitudinal Studies | Infant, Newborn | Cohort Studies
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Journal of Pediatric Gastroenterology and Nutrition, ISSN 0277-2116, 12/2016, Volume 63, Issue 6, pp. 577 - 578
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Journal of Pediatric Gastroenterology and Nutrition, ISSN 0277-2116, 01/2010, Volume 50, Issue 1, pp. 9 - 10
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The Journal of Pediatrics, ISSN 0022-3476, 09/2010, Volume 157, Issue 3, pp. 518 - 518
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Journal of Pediatrics, ISSN 0022-3476, 09/2010, Volume 157, Issue 3, p. 518
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