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1. Full Text Effectiveness of Immunoglobulin Replacement Therapy on Clinical Outcome in Patients with Primary Antibody Deficiencies: Results from a Multicenter Prospective Cohort Study
by Quinti, Isabella and Soresina, Annarosa and Guerra, Andrea and Rondelli, Roberto and Spadaro, Giuseppe and Agostini, Carlo and Milito, Cinzia and Trombetta, Amelia Chiara and Visentini, Marcella and Martini, Helene and Plebani, Alessandro and Fiorilli, Massimo and IPINet Investigators
Journal of Clinical Immunology, ISSN 0271-9142, 6/2011, Volume 31, Issue 3, pp. 315 - 322
A 5-years multicenter prospective study on 201 patients with common variable immunodeficiencies and 101 patients with X-linked agammaglobulinemia over a... 
effectiveness | Medical Microbiology | Immunoglobulin replacement | IgA | Biomedicine | Immunology | Internal Medicine | Infectious Diseases | common variable immunodeficiency | X-linked agammaglobulinemia | bronchiectasis | MANAGEMENT | EFFICACY | AGAMMAGLOBULINEMIA | IMMUNOLOGY | TRIAL | MEMORY B-CELLS | PRIMARY HYPOGAMMAGLOBULINEMIA | DOSE INTRAVENOUS IMMUNOGLOBULIN | LUNG-DISEASE | COMPLICATIONS | Common Variable Immunodeficiency - immunology | Agammaglobulinemia - immunology | Injections, Intravenous | Prospective Studies | Agammaglobulinemia - genetics | Common Variable Immunodeficiency - drug therapy | Follow-Up Studies | Humans | Middle Aged | Pneumonia - pathology | Child, Preschool | Infant | Male | Bronchiectasis - immunology | Incidence | Bronchiectasis - pathology | Agammaglobulinemia - pathology | Agammaglobulinemia - drug therapy | Genes, X-Linked | Common Variable Immunodeficiency - epidemiology | Immunoglobulin G - immunology | Pneumonia - immunology | Adult | Female | Child | Databases, Factual | Bronchiectasis - drug therapy | Comorbidity | Pneumonia - epidemiology | Risk Factors | Common Variable Immunodeficiency - pathology | Immunoglobulin G - therapeutic use | Treatment Outcome | Immunoglobulin G - administration & dosage | Disease-Free Survival | Pneumonia - drug therapy | Bronchiectasis - epidemiology | Immunoglobulin A - immunology | Adolescent | Italy | Aged | Agammaglobulinemia - epidemiology | Index Medicus
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2. Full Text X-Linked Agammagobulinemia in a Large Series of North African Patients: Frequency, Clinical Features and Novel BTK Mutations
by Aadam, Zahra and Kechout, Nadia and Barakat, Abdelhamid and Chan, Koon-Wing and Ben-Ali, Meriem and Ben-Mustapha, Imen and Zidi, Fethi and Ailal, Fatima and Attal, Nabila and Doudou, Fatouma and Abbadi, Mohamed-Cherif and Kaddache, Chawki and Smati, Leila and Touri, Nabila and Chemli, Jalel and Gargah, Tahar and Brini, Ines and Bakhchane, Amina and Charoute, Hicham and Jeddane, Leila and El Atiqi, Sara and El Hafidi, Naïma and Hida, Mustapha and Saile, Rachid and Alj, Hanane Salih and Boukari, Rachida and Bejaoui, Mohamed and Najib, Jilali and Barbouche, Mohamed-Ridha and Lau, Yu-Lung and Mellouli, Fethi and Bousfiha, Ahmed Aziz
Journal of Clinical Immunology, ISSN 0271-9142, 4/2016, Volume 36, Issue 3, pp. 187 - 194
X-linked agammagobulinemia (XLA) is a primary immunodeficiency caused by Bruton’s tyrosine kinase (BTK) gene defect. XLA patients have absent or reduced number... 
Medical Microbiology | north african population | Biomedicine | Immunology | novel mutations | BTK | Infectious Diseases | Internal Medicine | XLA | GENOTYPE-PHENOTYPE CORRELATION | GENE-MUTATIONS | GENOMIC ORGANIZATION | IMMUNOLOGY | IDENTIFICATION | B-CELLS | BRUTONS TYROSINE KINASE | FAMILIES | AGAMMAGLOBULINEMIA XLA | Agammaglobulinemia - immunology | Agammaglobulinemia - genetics | Humans | Child, Preschool | Genetic Diseases, X-Linked - complications | Agammaglobulinemia - diagnosis | Infant | Male | Genetic Counseling | Protein-Tyrosine Kinases - immunology | Protein-Tyrosine Kinases - genetics | Morocco | Adult | Genetic Diseases, X-Linked - genetics | Algeria | Opportunistic Infections - immunology | B-Lymphocytes - pathology | Child | Tunisia | Opportunistic Infections - complications | Gene Expression | Agammaglobulinemia - complications | Genetic Association Studies | Gene Frequency | Opportunistic Infections - genetics | Sequence Analysis, DNA | Genetic Diseases, X-Linked - diagnosis | Opportunistic Infections - diagnosis | Genetic Diseases, X-Linked - immunology | B-Lymphocytes - immunology | Age of Onset | Alleles | Heterozygote | Mutation | Genetic research | Genetic aspects | B cells | Index Medicus | Agammaglobulinemia/diagnosis | Protein-Tyrosine Kinases/genetics | Agammaglobulinemia/complications | Life Sciences | Agammaglobulinemia/genetics | Genetic Diseases, X-Linked/complications | Opportunistic Infections/complications | Biochemistry, Molecular Biology | Agammaglobulinemia/immunology | Genetic Diseases, X-Linked/immunology | B-Lymphocytes/pathology | Genetic Diseases, X-Linked/diagnosis | Opportunistic Infections/diagnosis | B-Lymphocytes/immunology | Protein-Tyrosine Kinases/immunology | Agammaglobulinaemia Tyrosine Kinase | Opportunistic Infections/immunology | Opportunistic Infections/genetics | Genetic Diseases, X-Linked/genetics
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3. Full Text Impact of trough IgG on pneumonia incidence in primary immunodeficiency: A meta-analysis of clinical studies
by Orange, Jordan S.|Grossman, William J.|Navickis, Roberta J.|Wilkes, Mahlon M
Clinical Immunology, ISSN 1521-6616, 2010, Volume 137, Issue 1, pp. 21 - 30
Abstract Primary immunodeficiency disease (PIDD) associated with hypogammaglobulinemia is typically treated with immunoglobulin replacement therapy. When... 
Allergy and Immunology | Pneumonia | Trough concentration | Common variable immunodeficiency | Intravenous immunoglobulin | IVIG | X-linked agammaglobulinemia | Dose | Incidence | Primary immunodeficiency | Meta-analysis | PRIMARY IMMUNE-DEFICIENCY | INTRAVENOUS GAMMA-GLOBULIN | EFFICACY | SAFETY | IMMUNOLOGY | PRIMARY HYPOGAMMAGLOBULINEMIA | DISEASES | IMMUNOGLOBULIN REPLACEMENT THERAPY | DOUBLE-BLIND | Agammaglobulinemia - immunology | Immunoglobulin G - blood | Humans | Middle Aged | Pneumonia - prevention & control | Child, Preschool | Immunoglobulins, Intravenous - administration & dosage | Infant | Male | Young Adult | Immunoglobulin G - immunology | Pneumonia - immunology | Adult | Female | Immunologic Deficiency Syndromes - blood | Immunoglobulins, Intravenous - blood | Immunologic Deficiency Syndromes - immunology | Agammaglobulinemia - prevention & control | Child | Immunologic Deficiency Syndromes - therapy | Agammaglobulinemia - complications | Immunologic Deficiency Syndromes - complications | Agammaglobulinemia - therapy | Treatment Outcome | Clinical Trials as Topic | Immunoglobulins, Intravenous - therapeutic use | Adolescent | Pneumonia - complications | Aged | Medicine, Experimental | Medical colleges | Medical research | Bacterial pneumonia | Immunoglobulin G | Hypogammaglobulinemia | Index Medicus
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4. Full Text Disseminated Spiroplasma apis Infection in Patient with Agammaglobulinemia, France
by Etienne, Nicolas and Etienne, Nicolas and Bret, Laurent and Bret, Laurent and Le Brun, Cécile and Le Brun, Cécile and Lecuyer, Hervé and Lecuyer, Hervé and Moraly, Josquin and Lanternier, Fanny and Lanternier, Fanny and Hermine, Olivier and Hermine, Olivier and Ferroni, Agnès and Ferroni, Agnès and Lecuit, Marc and Lecuit, Marc and Pereyre, Sabine and Pereyre, Sabine and Beven, Laure and Beven, Laure and Lortholary, Olivier and Lortholary, Olivier
Emerging infectious diseases, ISSN 1080-6040, 12/2018, Volume 24, Issue 12, pp. 2382 - 2386
We report a disseminated infection caused by Spiroplasma apis, a honeybee pathogen, in a patient in France who had X-linked agammaglobulinemia. Identification... 
genetic diseases | x linked agammaglobulinemia | agammaglobulinemia | bee | bacteria | insect stings | hypogammaglobulinemia | immunocompromised | Apis mellifera | bacterial endocarditis | bruton thyrosine kinase | btk | endocarditis | France | mycoplasma | septic arthritis | Apis | bacterial infection | Bruton | infective endocarditis | Spiroplasma apis | vector-borne infections | immunocompromised patient | Spiroplasma | hornet | INFECTIOUS DISEASES | IMMUNOLOGY | RNA, Ribosomal, 16S - metabolism | Skin - microbiology | Agammaglobulinemia - complications | Agammaglobulinemia - therapy | Humans | Genetic Diseases, X-Linked - complications | Agammaglobulinemia - diagnosis | Gram-Negative Bacterial Infections - drug therapy | Male | Treatment Outcome | Gram-Negative Bacterial Infections - microbiology | Spiroplasma - classification | Anti-Bacterial Agents - therapeutic use | Biopsy | Spiroplasma - genetics | Adult | Gram-Negative Bacterial Infections - diagnosis | Gram-Negative Bacterial Infections - etiology | Skin - pathology | Bacterial infections | Research | Agammaglobulinemia | Risk factors | Life Sciences | Human health and pathology | Microbiology and Parasitology | Infectious diseases | Emerging diseases | Bacteriology | Research Letter | Disseminated | Infection in Patient with Agammaglobulinemia, France
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5. Full Text Deleterious Mutations in LRBA Are Associated with a Syndrome of Immune Deficiency and Autoimmunity
by Lopez-Herrera, Gabriela and Tampella, Giacomo and Pan-Hammarström, Qiang and Herholz, Peer and Trujillo-Vargas, Claudia M and Phadwal, Kanchan and Simon, Anna Katharina and Moutschen, Michel and Etzioni, Amos and Mory, Adi and Srugo, Izhak and Melamed, Doron and Hultenby, Kjell and Liu, Chonghai and Baronio, Manuela and Vitali, Massimiliano and Philippet, Pierre and Dideberg, Vinciane and Aghamohammadi, Asghar and Rezaei, Nima and Enright, Victoria and Du, Likun and Salzer, Ulrich and Eibel, Hermann and Pfeifer, Dietmar and Veelken, Hendrik and Stauss, Hans and Lougaris, Vassilios and Plebani, Alessandro and Gertz, E. Michael and Schäffer, Alejandro A and Hammarström, Lennart and Grimbacher, Bodo
The American Journal of Human Genetics, ISSN 0002-9297, 06/2012, Volume 90, Issue 6, pp. 986 - 1001
Most autosomal genetic causes of childhood-onset hypogammaglobulinemia are currently not well understood. Most affected individuals are simplex cases, but both... 
B-LYMPHOCYTES | AUTOPHAGY GENE | PROTEIN | GRAY PLATELET SYNDROME | DISEASE | GENETICS & HEREDITY | X-LINKED AGAMMAGLOBULINEMIA | COMMON VARIABLE IMMUNODEFICIENCY | ENDOPLASMIC-RETICULUM | SELECTIVE IGA DEFICIENCY | LARGE COHORT | B-Lymphocytes - cytology | Cell Proliferation | Agammaglobulinemia - genetics | Microscopy, Electron, Transmission - methods | Humans | Autoimmunity - genetics | Child, Preschool | Genotype | Immunophenotyping | Male | Chromosome Mapping | Autophagy | Homozygote | Phenotype | Pedigree | Adaptor Proteins, Signal Transducing - genetics | Immunologic Deficiency Syndromes - genetics | Female | Models, Genetic | Mutation | Child | Apoptosis | Genetic Linkage | Autoimmunity | Gene mutations | Genetic susceptibility | Agammaglobulinemia | Causes of | Genetic aspects | Research | Immunoglobulins | Analysis | Immunodeficiency | Genetic research | Mitogens | Genotype & phenotype | Genetic disorders | Autoimmune diseases | Childrens health | Immune system | Index Medicus | Heredity | Hypogammaglobulinemia | Lipopolysaccharides | chromosome 4 | Cell activation | Lymphocytes B | Development | Genotypes | Phagocytosis | Linkage analysis
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6. Full Text Gastrointestinal Manifestations in X-linked Agammaglobulinemia
by Barmettler, Sara and Otani, Iris M and Minhas, Jasmit and Abraham, Roshini S and Chang, Yenhui and Dorsey, Morna J and Ballas, Zuhair K and Bonilla, Francisco A and Ochs, Hans D and Walter, Jolan E
Journal of Clinical Immunology, ISSN 0271-9142, 04/2017, Volume 37, Issue 3, pp. 287 - 294
X-linked agammaglobulinemia is a primary humoral immunodeficiency characterized by hypogammaglobulinemia and increased susceptibility to infection. Although... 
gastrointestinal manifestations | GI manifestations | Bruton’s agammaglobulinemia | BTK | enteritis | IBD | X-linked agammaglobulinemia | XLA | inflammatory bowel disease | GENOTYPE-PHENOTYPE CORRELATION | CROHNS-DISEASE | IMMUNOGLOBULIN | HUMANS | IMMUNOLOGY | Bruton's agammaglobulinemia | BRUTONS TYROSINE KINASE | INFLAMMATORY-BOWEL-DISEASE | THERAPY | IMMUNODEFICIENCY | Agammaglobulinemia - complications | Genetic Association Studies | Agammaglobulinemia - therapy | Humans | Gastrointestinal Diseases - etiology | Genetic Diseases, X-Linked - complications | Agammaglobulinemia - diagnosis | Immunophenotyping | Infant | Male | Gastrointestinal Diseases - diagnosis | Gastrointestinal Tract - pathology | Genetic Diseases, X-Linked - diagnosis | Lymphocyte Subsets - immunology | Lymphocyte Subsets - metabolism | Immunoglobulin Isotypes - blood | Phenotype | Pedigree | Aged, 80 and over | Biomarkers | Mutation | Genetic Diseases, X-Linked - therapy | Index Medicus
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7. Full Text Treatment of Chronic Enterovirus Encephalitis With Fluoxetine in a Patient With X-Linked Agammaglobulinemia
by Gofshteyn, Jacqueline, MD|Cárdenas, Ana María, PhD|Bearden, David, MD
Pediatric Neurology, ISSN 0887-8994, 2016, Volume 64, pp. 94 - 98
Abstract Introduction Enterovirus may result in a devastating chronic encephalitis in immunocompromised patients, particularly in patients with X-linked... 
Pediatrics | Neurology | fluoxetine | enterovirus | X-linked agammaglobulinemia | enterovirus encephalitis | SYSTEM | INFECTIONS | PERSISTENT | COXSACKIEVIRUS REPLICATION | PEDIATRICS | MENINGOENCEPHALITIS | INHIBITOR | CLINICAL NEUROLOGY | Enterovirus Infections - drug therapy | Agammaglobulinemia - complications | Antiviral Agents - therapeutic use | Encephalitis, Viral - diagnostic imaging | Humans | Child, Preschool | Genetic Diseases, X-Linked - complications | Male | Encephalitis, Viral - complications | Encephalitis, Viral - drug therapy | Enterovirus Infections - diagnostic imaging | Agammaglobulinemia - pathology | Agammaglobulinemia - drug therapy | Genetic Diseases, X-Linked - drug therapy | Enterovirus Infections - complications | Agammaglobulinemia - diagnostic imaging | Genetic Diseases, X-Linked - pathology | Genetic Diseases, X-Linked - diagnostic imaging | Encephalitis, Viral - pathology | Enterovirus Infections - pathology | Fluoxetine - therapeutic use | Chronic Disease | Encephalitis | Antiviral agents | Care and treatment | Fluoxetine | Agammaglobulinemia | Mortality | Drug approval | Index Medicus
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8. Full Text Agammaglobulinemia and absent B lineage cells in a patient lacking the p85α subunit of PI3K
by Conley, Mary Ellen and Dobbs, A. Kerry and Quintana, Anita M and Bosompem, Amma and Wang, Yong-Dong and Coustan-Smith, Elaine and Smith, Amber M and Perez, Elena E and Murray, Peter J
Journal of Experimental Medicine, ISSN 0022-1007, 03/2012, Volume 209, Issue 3, pp. 463 - 470
Whole exome sequencing was used to determine the causative gene in patients with B cell defects of unknown etiology. A homozygous premature stop codon in exon... 
MEDICINE, RESEARCH & EXPERIMENTAL | BRUTONS TYROSINE KINASE | COMPLEX | PROTEIN | X-LINKED AGAMMAGLOBULINEMIA | PHOSPHOINOSITIDE 3-KINASE P110-DELTA | RECEPTOR | CXCR4 | MICE | IMMUNOLOGY | EXPRESSION | ANTIGEN | Agammaglobulinemia - immunology | Agammaglobulinemia - genetics | Exons | Dendritic Cells - immunology | Humans | Male | Case-Control Studies | Young Adult | Cell Differentiation - genetics | Agammaglobulinemia - enzymology | Class Ia Phosphatidylinositol 3-Kinase - deficiency | DNA Mutational Analysis | Base Sequence | Female | B-Lymphocytes - pathology | Class Ia Phosphatidylinositol 3-Kinase - genetics | Amino Acid Sequence | B-Lymphocytes - enzymology | Codon, Nonsense | Mice, Knockout | Homozygote | Animals | B-Lymphocytes - immunology | Pedigree | Mice | Cytokines - biosynthesis | Index Medicus | Brief Definitive Report
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9. Full Text Update on the safety and efficacy of retroviral gene therapy for immunodeficiency due to adenosine deaminase deficiency
by Cicalese, Maria Pia and Ferrua, Francesca and Castagnaro, Laura and Pajno, Roberta and Barzaghi, Federica and Giannelli, Stefania and Dionisio, Francesca and Brigida, Immacolata and Bonopane, Marco and Casiraghi, Miriam and Tabucchi, Antonella and Carlucci, Filippo and Grunebaum, Eyal and Adeli, Mehdi and Bredius, Robbert G and Puck, Jennifer M and Stepensky, Polina and Tezcan, Ilhan and Rolfe, Katie and De Boever, Erika and Reinhardt, Rickey R and Appleby, Jonathan and Ciceri, Fabio and Roncarolo, Maria Grazia and Aiuti, Alessandro
Blood, ISSN 0006-4971, 07/2016, Volume 128, Issue 1, pp. 45 - 54
Adenosine deaminase (ADA) deficiency is a rare, autosomal-recessive systemic metabolic disease characterized by severe combined immunodeficiency (SCID). The... 
BONE-MARROW-TRANSPLANTATION | COMBINED IMMUNE-DEFICIENCY | REPLACEMENT THERAPY | ANTIBODY | EXPERIENCE | STEM-CELL TRANSPLANTATION | HEMATOLOGY | RECONSTITUTION | ADA | CHILDREN | LYMPHOCYTES | Genetic Therapy | Agammaglobulinemia - immunology | Agammaglobulinemia - genetics | Humans | Severe Combined Immunodeficiency - mortality | Child, Preschool | Infant | Male | Recovery of Function | CD4-Positive T-Lymphocytes - immunology | Female | Adenosine Deaminase - deficiency | Child | Adenosine Deaminase - genetics | Agammaglobulinemia - therapy | Agammaglobulinemia - mortality | Retroviridae | Severe Combined Immunodeficiency - therapy | Survival Rate | Severe Combined Immunodeficiency - immunology | Disease-Free Survival | Severe Combined Immunodeficiency - genetics | B-Lymphocytes - immunology | CD8-Positive T-Lymphocytes - immunology | Adenosine Deaminase - immunology | Index Medicus | Abridged Index Medicus | 100 | Gene Therapy
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10. Full Text Progressive Neurodegenerative Syndrome in a Patient with X-Linked Agammaglobulinemia Receiving Intravenous Immunoglobulin Therapy
by Sag, AT and Saka, E and Ozgur, TT and Sanal, O and Ayvaz, DC and Elibol, B and Kurne, AT
COGNITIVE AND BEHAVIORAL NEUROLOGY, ISSN 1543-3633, 09/2014, Volume 27, Issue 3, pp. 155 - 159
A progressive encephalopathy of unknown etiology has been described in patients with primary immunodeficiency disorders. In this report, we characterize the... 
CELLS | AUTOIMMUNITY | Bruton agammaglobulinemia | DISEASE | neurodegeneration | BEHAVIORAL SCIENCES | immunodeficiency | X-linked agammaglobulinemia | CLINICAL NEUROLOGY | Neurodegenerative Diseases - etiology | Humans | Immunoglobulins, Intravenous - adverse effects | Movement Disorders - immunology | Child, Preschool | Genetic Diseases, X-Linked - complications | Immunoglobulins, Intravenous - administration & dosage | Agammaglobulinemia - diagnosis | Male | Atrophy | Young Adult | Agammaglobulinemia - pathology | Agammaglobulinemia - drug therapy | Genetic Diseases, X-Linked - drug therapy | Cognition Disorders - etiology | Cognition Disorders - immunology | Genetic Diseases, X-Linked - physiopathology | Diagnosis, Differential | Agammaglobulinemia - complications | Cognition Disorders - genetics | Disease Progression | Genetic Diseases, X-Linked - diagnosis | Agammaglobulinemia - physiopathology | Neuropsychological Tests | Magnetic Resonance Imaging | Agammaglobulinemia - psychology | Movement Disorders - etiology | Brain - pathology | Genetic Diseases, X-Linked - pathology | Movement Disorders - genetics | Genetic Diseases, X-Linked - psychology | Frontal Lobe - pathology | Index Medicus
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11. Full Text CPID 6: ACUTE PRE‐B LYMPHOBLASTIC LEUKAEMIA IN A PATIENT WITH X‐LINKED AGAMMAGLOBULINEMIA
by Pumar, M and Fong, CY and Aui, PM and van Zelm, MC and Bosco, J
Internal Medicine Journal, ISSN 1444-0903, 09/2017, Volume 47, Issue S5, pp. 39 - 39
Leukemia | X-linked agammaglobulinemia | Agammaglobulinemia
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12. Full Text Clinical and mutational features of X-linked agammaglobulinemia in Mexico
by García-García, E.|Staines-Boone, A.T.|Vargas-Hernández, A.|González-Serrano, M.E.|Carrillo-Tapia, E.|Mogica-Martínez, D.|Berrón-Ruíz, L.|Segura-Mendez, N.H.|Espinosa-Rosales, F.J.|Yamazaki-Nakashimada, M.A.|Santos-Argumedo, L.|López-Herrera, G
Clinical Immunology, ISSN 1521-6616, 2015, Volume 165, pp. 38 - 44
Abstract X-linked agammaglobulinemia (XLA) is caused by BTK mutations, patients typically show < 2% of peripheral B cells and reduced levels of all... 
Allergy and Immunology | Missense mutations | Btk | X-linked agammaglobulinemia | Splice site | BRUTONS TYROSINE KINASE | STIMULATION | PROTEIN | GENE | IMMUNOLOGY | EXPRESSION | MOLECULAR ANALYSIS | Agammaglobulinemia - complications | Agammaglobulinemia - genetics | Immunoglobulin G - blood | Humans | Immunoglobulin A - genetics | Genetic Diseases, X-Linked - complications | Agammaglobulinemia - diagnosis | Genetic Diseases, X-Linked - diagnosis | Mutation, Missense - genetics | Agammaglobulinemia - pathology | Immunoglobulin G - genetics | Immunoglobulin M - blood | Arthritis - complications | Genetic Diseases, X-Linked - pathology | Immunoglobulin A - blood | Genetic Diseases, X-Linked - genetics | Mexico | Immunoglobulin M - genetics | Virus diseases | Development and progression | Genetic aspects | Arthritis | B cells | Agammaglobulinemia | Rheumatoid factor | Medical research | Medicine, Experimental | Index Medicus
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13. Full Text Autoimmunity and Inflammation in X-linked Agammaglobulinemia
by Hernandez-Trujillo, Vivian P and Scalchunes, Chris and Cunningham-Rundles, Charlotte and Ochs, Hans D and Bonilla, Francisco A and Paris, Ken and Yel, Leman and Sullivan, Kathleen E
Journal of Clinical Immunology, ISSN 0271-9142, 8/2014, Volume 34, Issue 6, pp. 627 - 632
In the past, XLA was described as associated with several inflammatory conditions, but with adequate immune globulin treatment, these are presumed to have... 
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