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American journal of medical genetics. Part A, ISSN 1552-4825, 11/2017, Volume 173, Issue 11, pp. 2912 - 2922
KMT2D gene | Kabuki syndrome | KDM6A gene | congenital heart defect | Life Sciences & Biomedicine | Genetics & Heredity | Science & Technology | Aortic Valve Stenosis - genetics | Vestibular Diseases - complications | Aortic Valve - abnormalities | Face - abnormalities | Humans | Male | Heart Septal Defects, Ventricular - physiopathology | Heart Septal Defects, Atrial - physiopathology | Histone Demethylases - genetics | Aortic Coarctation - physiopathology | Heart Defects, Congenital - genetics | Aortic Coarctation - complications | Female | Heart Septal Defects, Atrial - genetics | Vestibular Diseases - physiopathology | Neoplasm Proteins - genetics | Nuclear Proteins - genetics | Abnormalities, Multiple - genetics | Heart Valve Diseases - physiopathology | Hematologic Diseases - complications | Heart Septal Defects, Ventricular - genetics | Aortic Valve Stenosis - physiopathology | Aortic Valve - physiopathology | DNA-Binding Proteins - genetics | Abnormalities, Multiple - physiopathology | Face - physiopathology | Aortic Valve Stenosis - complications | Heart Defects, Congenital - complications | Hematologic Diseases - physiopathology | Heart Valve Diseases - genetics | Hematologic Diseases - genetics | Aortic Coarctation - genetics | Heart Defects, Congenital - physiopathology | Vestibular Diseases - genetics | Heart | Congenital heart disease | Genetic disorders | Coronary heart disease | Echocardiography | Congenital defects | Aortic arch | Aorta | Ventricle | Health risk assessment | Aortic valve | Defects | Index Medicus
Journal Article
Arteriosclerosis, thrombosis, and vascular biology, ISSN 1079-5642, 11/2014, Volume 34, Issue 11, pp. 2387 - 2393
Calcification | Aortic valve stenosis | Inflammation | Peripheral Vascular Disease | Life Sciences & Biomedicine | Hematology | Cardiovascular System & Cardiology | Science & Technology | Heart Valve Diseases - physiopathology | Calcinosis - diagnosis | Heart Valve Prosthesis Implantation | Humans | Aortic Valve Stenosis - physiopathology | Aortic Valve - physiopathology | Biomedical Research - trends | Aortic Valve Stenosis - diagnosis | Aortic Valve Stenosis - therapy | Hemodynamics - physiology | Aortic Valve - pathology | Calcinosis - therapy | Cardiac Surgical Procedures | Heart Defects, Congenital - diagnosis | Heart Valve Diseases - therapy | Signal Transduction - physiology | Heart Defects, Congenital - physiopathology | Heart Defects, Congenital - therapy | Heart Valve Diseases - diagnosis | Calcinosis - physiopathology | Index Medicus | aortic stenosis | calcification | Calcific aortic valve disease | inflammation
Journal Article
Ultrasound in obstetrics & gynecology, ISSN 0960-7692, 12/2019, Volume 54, Issue 6, pp. 780 - 785
left heart hypoplasia | fetal echocardiogram | altered hemodynamics | lower urinary tract obstruction | Acoustics | Life Sciences & Biomedicine | Technology | Radiology, Nuclear Medicine & Medical Imaging | Obstetrics & Gynecology | Science & Technology | Aorta - abnormalities | Cardiac Output - physiology | Lower Urinary Tract Symptoms - complications | Humans | Echocardiography - methods | Cardiomegaly - epidemiology | Fetal Heart - diagnostic imaging | Hemodynamics - physiology | Hypertrophy, Left Ventricular - epidemiology | Mitral Valve - physiopathology | Hypertrophy, Right Ventricular - physiopathology | Aortic Valve Stenosis - epidemiology | Fetal Death | Urethral Obstruction - diagnostic imaging | Hypoplastic Left Heart Syndrome - epidemiology | Adult | Female | Ultrasonography, Prenatal - methods | Retrospective Studies | Aorta - physiopathology | Hypertrophy, Right Ventricular - epidemiology | Fetal Heart - physiology | Ventricular Dysfunction, Left - epidemiology | Aorta - diagnostic imaging | Abortion, Induced - statistics & numerical data | Pericardial Effusion - physiopathology | Aortic Valve Stenosis - physiopathology | Cardiomegaly - physiopathology | Lower Urinary Tract Symptoms - physiopathology | Ventricular Dysfunction, Left - diagnosis | Fetal Diseases - diagnostic imaging | Hypoplastic Left Heart Syndrome - physiopathology | Gestational Age | Lower Urinary Tract Symptoms - embryology | Ventricular Dysfunction, Left - physiopathology | Pericardial Effusion - epidemiology | Pregnancy | Fetal Diseases - physiopathology | Mitral Valve - diagnostic imaging | Hypertrophy, Left Ventricular - physiopathology | Urethral Obstruction - complications | Urethral Obstruction - embryology | Mitral Valve - abnormalities | Heart | Stenosis | Bladder | Infants | Urinary tract | Gestational age | Ultrasonic imaging | Electrocardiography | Aorta | Rheumatic heart disease | Urogenital system | Heart diseases | Hypoplasia | Performance indices | Mitral valve | Echocardiography | Effusion | Fetuses | Abnormalities | Disease control | Coronary artery disease | Heart valves | Aortic arch | Hemodynamics | Ventricle | Cardiac output | Inflow | Cardiovascular diseases | Hypertrophy | Structure-function relationships | Index Medicus
Journal Article
JACC. Cardiovascular interventions, ISSN 1936-8798, 10/2018, Volume 11, Issue 20, pp. 2019 - 2031
instantaneous wave-free ratio | aortic stenosis | coronary flow | fractional flow reserve | TAVR | Cardiac & Cardiovascular Systems | Life Sciences & Biomedicine | Cardiovascular System & Cardiology | Science & Technology | Predictive Value of Tests | Humans | Male | Cardiac Catheterization | Sweden | Coronary Artery Disease - physiopathology | Aged, 80 and over | Female | Aortic Valve Stenosis - surgery | Transcatheter Aortic Valve Replacement - adverse effects | Severity of Illness Index | Coronary Stenosis - complications | Reproducibility of Results | Aortic Valve Stenosis - physiopathology | Treatment Outcome | Aortic Valve Stenosis - diagnosis | Aortic Valve Stenosis - complications | Fractional Flow Reserve, Myocardial | Coronary Artery Disease - diagnosis | Coronary Artery Disease - complications | Coronary Stenosis - physiopathology | Hyperemia - physiopathology | Blood Flow Velocity | London | Aged | Hemodynamics | Coronary Stenosis - diagnosis
Journal Article
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Full Text
Two decades of experience with root remodeling and valve repair for bicuspid aortic valves
The Journal of thoracic and cardiovascular surgery, ISSN 0022-5223, 2017, Volume 153, Issue 4, pp. S65 - S71
Cardiothoracic Surgery | root remodeling | aortic root replacement | bicuspid aortic valve | aortic valve repair | Cardiac & Cardiovascular Systems | Respiratory System | Life Sciences & Biomedicine | Cardiovascular System & Cardiology | Surgery | Science & Technology | Recurrence | Humans | Middle Aged | Cardiac Valve Annuloplasty - mortality | Male | Aortic Valve - surgery | Young Adult | Aneurysm, Dissecting - physiopathology | Time Factors | Aneurysm, Dissecting - surgery | Aged, 80 and over | Heart Valve Diseases - mortality | Pericardium - transplantation | Child | Dilatation, Pathologic | Heart Valve Diseases - physiopathology | Reoperation | Risk Factors | Heart Valve Prosthesis Implantation - mortality | Aortic Valve Insufficiency - etiology | Bicuspid Aortic Valve Disease | Aorta - surgery | Adolescent | Aneurysm, Dissecting - mortality | Vascular Remodeling | Aortic Valve - abnormalities | Heart Valve Diseases - surgery | Aortic Aneurysm - etiology | Heart Valve Diseases - complications | Aortic Valve Stenosis - etiology | Adult | Female | Aortic Valve Stenosis - surgery | Retrospective Studies | Aorta - physiopathology | Cardiac Valve Annuloplasty - adverse effects | Aneurysm, Dissecting - etiology | Hospital Mortality | Aortic Aneurysm - mortality | Aortic Aneurysm - physiopathology | Aortic Valve Stenosis - physiopathology | Aortic Aneurysm - surgery | Aortic Valve - physiopathology | Aortic Valve Insufficiency - physiopathology | Treatment Outcome | Heart Valve Prosthesis Implantation - adverse effects | Aortic Valve Insufficiency - surgery | Aged | Aortic Valve Insufficiency - mortality | Aneurysms | Heart valve diseases | Epidemiology | Medical informatics | Health aspects
Journal Article
JACC. Cardiovascular interventions, ISSN 1936-8798, 10/2017, Volume 10, Issue 20, pp. 2050 - 2060
in-hospital mortality | major adverse cardiovascular event(s) | transcatheter aortic valve replacement | chronic kidney disease | acute kidney injury | end-stage renal disease | Cardiac & Cardiovascular Systems | Life Sciences & Biomedicine | Cardiovascular System & Cardiology | Science & Technology | Kidney Failure, Chronic - mortality | Multivariate Analysis | United States - epidemiology | Humans | Male | Aortic Valve - surgery | Aortic Valve Stenosis - diagnostic imaging | Aortic Valve Stenosis - mortality | Incidence | Renal Insufficiency, Chronic - therapy | Time Factors | Aged, 80 and over | Renal Insufficiency, Chronic - mortality | Female | Renal Insufficiency, Chronic - diagnosis | Aortic Valve Stenosis - surgery | Retrospective Studies | Odds Ratio | Kidney - physiopathology | Databases, Factual | Transcatheter Aortic Valve Replacement - adverse effects | Kidney Failure, Chronic - physiopathology | Kidney Failure, Chronic - diagnosis | Aortic Valve - diagnostic imaging | Hospital Mortality | Risk Factors | Aortic Valve Stenosis - physiopathology | Aortic Valve - physiopathology | Linear Models | Logistic Models | Treatment Outcome | Chi-Square Distribution | Acute Kidney Injury - physiopathology | Renal Insufficiency, Chronic - physiopathology | Kidney Failure, Chronic - therapy | Acute Kidney Injury - mortality | Acute Kidney Injury - therapy | Aged | Transcatheter Aortic Valve Replacement - mortality | Renal Dialysis | Index Medicus
Journal Article
Hypertension (Dallas, Tex. 1979), ISSN 0194-911X, 06/2012, Volume 59, Issue 6, pp. 1170 - 1178
Transverse aortic constriction | Pulmonary vascular morphology | Pulmonary hypertension | Peripheral Vascular Disease | Life Sciences & Biomedicine | Cardiovascular System & Cardiology | Science & Technology | Cardiology. Vascular system | Biological and medical sciences | Arterial hypertension. Arterial hypotension | Medical sciences | Clinical manifestations. Epidemiology. Investigative techniques. Etiology | Blood and lymphatic vessels | Leukocytes - pathology | Lung Diseases - metabolism | Heart Failure - physiopathology | Hypertension, Pulmonary - physiopathology | Ventricular Dysfunction, Left - complications | Male | Pulmonary Edema - etiology | Lung Diseases - etiology | Pulmonary Edema - physiopathology | Collagen - genetics | Lung - metabolism | Pulmonary Edema - metabolism | Heart Failure - complications | Lung - pathology | Hypertrophy, Left Ventricular - metabolism | Mice, Inbred C57BL | Water - metabolism | Organ Size | Heart Failure - metabolism | Hypertension, Pulmonary - metabolism | Lung - physiopathology | Reverse Transcriptase Polymerase Chain Reaction | Constriction, Pathologic - complications | Blotting, Western | Ventricular Dysfunction, Left - physiopathology | Aorta - pathology | Ventricular Dysfunction, Left - metabolism | Collagen - metabolism | Animals | Transforming Growth Factor beta - genetics | Fibrosis - etiology | Hypertrophy, Left Ventricular - complications | Hypoxia - physiopathology | Lung Diseases - physiopathology | Mice | Hypertrophy, Left Ventricular - physiopathology | Hypertension, Pulmonary - etiology | Leukocytes - metabolism | Transforming Growth Factor beta - metabolism | Index Medicus | transverse aortic constriction | pulmonary hypertension | pulmonary vascular morphology
Journal Article
The American journal of cardiology, ISSN 0002-9149, 08/2020, Volume 128, pp. 210 - 215
Cardiac & Cardiovascular Systems | Life Sciences & Biomedicine | Cardiovascular System & Cardiology | Science & Technology | Aortic Diseases - diagnostic imaging | Age Factors | Aortic Valve - abnormalities | Humans | Middle Aged | Dilatation, Pathologic - physiopathology | Male | Asymptomatic Diseases | Hypertrophy, Left Ventricular - epidemiology | Case-Control Studies | Cause of Death | Aortic Valve Stenosis - diagnostic imaging | Aortic Valve Stenosis - epidemiology | Heart Valve Diseases - epidemiology | Heart Valve Diseases - complications | Aged, 80 and over | Adult | Female | Retrospective Studies | Dilatation, Pathologic - diagnostic imaging | Severity of Illness Index | Heart Valve Diseases - physiopathology | Echocardiography | Aortic Diseases - epidemiology | Aortic Valve - diagnostic imaging | Mortality | Risk Factors | Aortic Valve Stenosis - physiopathology | Kaplan-Meier Estimate | Proportional Hazards Models | Aortic Valve - physiopathology | Bicuspid Aortic Valve Disease | Stroke Volume | Heart Valve Prosthesis Implantation - statistics & numerical data | Aortic Diseases - physiopathology | Aortic Valve Stenosis - complications | Dilatation, Pathologic - epidemiology | Aged | Hypertrophy, Left Ventricular - physiopathology | Heart Valve Diseases - diagnostic imaging | Hypertrophy, Left Ventricular - diagnostic imaging | Heart | Stenosis | Cardiovascular disease | Risk factors | Subgroups | Confidence intervals | Aorta | Hypertension | Stroke | Diabetes mellitus | Health risks | Risk analysis | Mathematical morphology | Heart valves | Morbidity | Studies | Geometry | Survival analysis | Statistical models | Morphology | Health hazards | Dilation | Diabetes | Kidney diseases | Ventricle | Cardiovascular diseases | Aortic valve | Hypertrophy | Ejection fraction | Index Medicus | Abridged Index Medicus
Journal Article
Trends in cardiovascular medicine, ISSN 1050-1738, 02/2019, Volume 29, Issue 2, pp. 61 - 68
NOTCH signaling | Aortopathy | Cell differentiation | Vascular smooth muscle cells | Bicuspid aortic valve | Cardiac & Cardiovascular Systems | Life Sciences & Biomedicine | Cardiovascular System & Cardiology | Science & Technology | Prognosis | Heart Valve Diseases - pathology | Muscle, Smooth, Vascular - metabolism | Aortic Valve - abnormalities | Humans | Myocytes, Smooth Muscle - pathology | Aorta - metabolism | Muscle, Smooth, Vascular - physiopathology | Aortic Diseases - metabolism | Aortic Valve - pathology | Cell Differentiation | Aorta - physiopathology | Myocytes, Smooth Muscle - metabolism | Aortic Diseases - pathology | Heart Valve Diseases - physiopathology | Genetic Predisposition to Disease | Signal Transduction | Vasoconstriction | Aortic Valve - physiopathology | Receptor, Notch1 - metabolism | Aortic Valve - metabolism | Bicuspid Aortic Valve Disease | Disease Progression | Aorta - pathology | Aortic Diseases - genetics | Aortic Diseases - physiopathology | Muscle, Smooth, Vascular - pathology | Phenotype | Animals | Heart Valve Diseases - metabolism | Heart Valve Diseases - genetics | Mutation | Receptor, Notch1 - genetics | Apoptosis | Congenital diseases | Homeostasis | Aneurysms | Smooth muscle | Gene expression | Muscle contraction | Coronary artery disease | Cell adhesion & migration | Proteins | Genotype & phenotype | Coronary vessels | Gangrene | Aorta | Extracellular matrix | Protein expression | Ligands | Physiology | Genetic engineering | Heart diseases | Dissection | Aortic valve | Index Medicus
Journal Article