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The New England journal of medicine, ISSN 1533-4406, 2017, Volume 377, Issue 21, pp. 2024 - 2035
Journal Article
The New England journal of medicine, ISSN 1533-4406, 2011, Volume 365, Issue 18, pp. 1663 - 1672
Journal Article
The New England journal of medicine, ISSN 1533-4406, 2017, Volume 377, Issue 21, pp. 2013 - 2023
Journal Article
American journal of respiratory cell and molecular biology, ISSN 1044-1549, 01/2017, Volume 56, Issue 1, pp. 99 - 108
Acquired cystic fibrosis transmembrane conductance regulator (CFTR) dysfunction may contribute to chronic obstructive pulmonary disease pathogenesis and is a potential therapeutic target... 
Cystic fibrosis transmembrane conductance regulator potentiator | Ivacaftor | Optical coherence tomography | Cigarette smoke | Mucociliary transport | ACTIVATION | BRONCHIAL EPITHELIAL-CELLS | optical coherence tomography | BIOCHEMISTRY & MOLECULAR BIOLOGY | cystic fibrosis transmembrane conductance regulator potentiator | ivacaftor | cigarette smoke | FUNCTION IN-VITRO | mucociliary transport | CELL BIOLOGY | AIRWAY | RESPIRATORY SYSTEM | SECRETION | DYSFUNCTION | MUTATIONS | EXPRESSION | RESIDUES | CFTR | Cystic Fibrosis Transmembrane Conductance Regulator - antagonists & inhibitors | Smoking - adverse effects | Acrolein - pharmacology | Amino Acid Sequence | Epithelial Cells - metabolism | Tomography, Optical Coherence | Epithelial Cells - drug effects | Humans | Cells, Cultured | Cystic Fibrosis Transmembrane Conductance Regulator - metabolism | Quinolones - pharmacology | Cystic Fibrosis Transmembrane Conductance Regulator - chemistry | Aminophenols - pharmacology | Cilia - metabolism | Mucociliary Clearance - drug effects | Trachea - pathology | Mucous Membrane - pathology | Cilia - drug effects | Bronchi - pathology | Ion Channel Gating - drug effects | Proteins | Studies | Genotype & phenotype | Tomography | Cystic fibrosis | Software | Chronic obstructive pulmonary disease | Bronchitis | Kinases | Cigarettes
Journal Article
The New England journal of medicine, ISSN 1533-4406, 2018, Volume 379, Issue 17, pp. 1599 - 1611
Journal Article
The New England journal of medicine, ISSN 1533-4406, 2015, Volume 373, Issue 3, pp. 220 - 231
Journal Article
American journal of respiratory and critical care medicine, ISSN 1535-4970, 2013, Volume 188, Issue 11, pp. 1321 - 1330
Journal Article
The New England journal of medicine, ISSN 1533-4406, 2018, Volume 379, Issue 17, pp. 1612 - 1620
BACKGROUND: VX-445 is a next-generation cystic fibrosis transmembrane conductance regulator (CFTR... 
G551D MUTATION | MEDICINE, GENERAL & INTERNAL | TEZACAFTOR-IVACAFTOR | CFTR | Pyrazoles - therapeutic use | Forced Expiratory Volume - drug effects | Humans | Pyrrolidines - administration & dosage | Chloride Channel Agonists - therapeutic use | Male | Aminophenols - therapeutic use | Chloride Channel Agonists - adverse effects | Aminophenols - adverse effects | Pyrrolidines - pharmacology | Pyrrolidines - therapeutic use | Sweat - chemistry | Young Adult | Quinolones - adverse effects | Chlorides - metabolism | Quinolones - therapeutic use | Adult | Benzodioxoles - adverse effects | Female | Benzodioxoles - therapeutic use | Pyrazoles - pharmacology | Pyridines - therapeutic use | Pyridines - administration & dosage | Double-Blind Method | Genotype | Cystic Fibrosis Transmembrane Conductance Regulator - metabolism | Chlorides - analysis | Pyrazoles - administration & dosage | Indoles - adverse effects | Cystic Fibrosis - genetics | Adolescent | Alleles | Cystic Fibrosis Transmembrane Conductance Regulator - genetics | Indoles - therapeutic use | Pyridines - pharmacology | Mutation | Cystic Fibrosis - drug therapy | Drug Combinations | Cystic fibrosis | Ivacaftor | Dosage and administration | Drug therapy | Statistical analysis | Writers | Epithelial cells | Chloride transport | Recovery of function | Patients | Design | Proteins | Genotype & phenotype | Chloride | Collaboration | Conductance | Cystic fibrosis transmembrane conductance regulator | Protein transport | Sweat | Pharmaceuticals
Journal Article