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Blood, ISSN 0006-4971, 07/2017, Volume 130, Issue 2, pp. 167 - 175
Langerhans cell histiocytosis (LCH) and Erdheim-Chester disease (ECD) are rare histiocytic disorders induced by somatic mutation of MAPK pathway genes.... 
MANAGEMENT | DENDRITIC CELLS | NEOPLASMS | DISTINCT | MONOCYTES | SUBSETS | NOTCH | MUTATIONS | MATURATION | HEMATOLOGY | BLOOD | Antigens, CD - immunology | Dendritic Cells - immunology | Histiocytosis, Langerhans-Cell - diagnosis | Histiocytosis, Langerhans-Cell - genetics | Humans | Lectins, C-Type - immunology | Dendritic Cells - pathology | Hematopoietic Stem Cells - pathology | Erdheim-Chester Disease - immunology | Male | Receptors, Notch - genetics | Monocytes - immunology | Lectins, C-Type - genetics | Antigens, CD - genetics | Hematopoietic Stem Cells - immunology | Histiocytosis, Langerhans-Cell - pathology | Bone Marrow Cells - immunology | Monocytes - pathology | Adult | Female | Cell Differentiation | Foam Cells - pathology | Glycoproteins - genetics | Transforming Growth Factor beta - immunology | Antigens, CD1 - immunology | Diagnosis, Differential | Erdheim-Chester Disease - genetics | Gene Expression | Bone Marrow Cells - pathology | Immunophenotyping | Lipopolysaccharide Receptors - immunology | Histiocytosis, Langerhans-Cell - immunology | Erdheim-Chester Disease - pathology | Granulocyte-Macrophage Colony-Stimulating Factor - genetics | Glycoproteins - immunology | Granulocyte-Macrophage Colony-Stimulating Factor - immunology | Mannose-Binding Lectins - genetics | Mannose-Binding Lectins - immunology | Transforming Growth Factor beta - genetics | Proto-Oncogene Proteins B-raf - genetics | Proto-Oncogene Proteins B-raf - immunology | Alleles | Erdheim-Chester Disease - diagnosis | Lipopolysaccharide Receptors - genetics | Foam Cells - immunology | Antigens, CD1 - genetics | Mutation | Receptors, Notch - immunology | Myeloid Neoplasia
Journal Article
Nature, ISSN 0028-0836, 09/2017, Volume 549, Issue 7672, pp. 389 - 393
The pathophysiology of neurodegenerative diseases is poorly understood and there are few therapeutic options. Neurodegenerative diseases are characterized by... 
DENDRITIC CELLS | PATTERN | LANGERHANS CELL HISTIOCYTOSIS | ALZHEIMERS-DISEASE | MULTIDISCIPLINARY SCIENCES | KINASE | MICE | MODEL | ERDHEIM-CHESTER-DISEASE | EXPRESSION | Microglia - metabolism | Clone Cells - enzymology | Humans | Male | Myeloid Progenitor Cells - enzymology | Extracellular Signal-Regulated MAP Kinases - metabolism | MAP Kinase Signaling System | Erythroid Precursor Cells - enzymology | Histiocytosis - pathology | Microglia - pathology | Female | Proto-Oncogene Proteins B-raf - metabolism | Disease Models, Animal | Histiocytosis - enzymology | Myeloid Progenitor Cells - metabolism | Neurodegenerative Diseases - pathology | Macrophages - pathology | Microglia - enzymology | Neurodegenerative Diseases - genetics | Myeloid Progenitor Cells - pathology | Histiocytosis - metabolism | Neurodegenerative Diseases - metabolism | Clone Cells - metabolism | Macrophages - enzymology | Proto-Oncogene Proteins B-raf - antagonists & inhibitors | Erythroid Precursor Cells - pathology | Macrophages - metabolism | Animals | Clone Cells - pathology | Proto-Oncogene Proteins B-raf - genetics | Histiocytosis - genetics | Erythroid Precursor Cells - metabolism | Mosaicism | Mice | Mutation | Neurodegenerative Diseases - enzymology | Physiological aspects | Nervous system | Development and progression | Degeneration | Genetic aspects | Research | Histiocytosis | Mitogen-activated protein kinases | Intervention | Disease | Stem cell transplantation | Activation | Genomes | Kinases | Macrophages | Neuronal-glial interactions | Genotype & phenotype | Allografts | Neurodegeneration | Rodents | Bone marrow | Ataxia | Alzheimer's disease | Myeloid cells | Cytokines | Neurodegenerative diseases | Fetuses | Extracellular signal-regulated kinase | MAP kinase | Cell lineage | Gene expression | Patients | Amyloid precursor protein | Microglia | Organogenesis | Diseases | Neurological diseases | Gliosis | Stem cells | Neural stem cells
Journal Article
Modern Pathology, ISSN 0893-3952, 04/2018, Volume 31, Issue 4, pp. 581 - 597
Erdheim-Chester disease is a rare, non-Langerhans cell histiocytosis histologically characterized by multi-systemic proliferation of mature histiocytes in a... 
KINASE ALTERATIONS | MUTATIONS | PATHOLOGY | Erdheim-Chester Disease - genetics | Humans | Erdheim-Chester Disease - pathology | Cohort Studies | Retroperitoneum | Oral cavity | Biopsy | Stroma | Bone marrow | Mutation | Histiocytosis | Heart diseases
Journal Article
Journal Article
Journal Article
Cardiology Clinics, ISSN 0733-8651, 11/2017, Volume 35, Issue 4, pp. 589 - 600
Pericardial tumors are rare lesions that include a range of neoplastic conditions that may arise within the pericardium or metastasize to involve it... 
Masses | Epicardium | Thoracic | Cardiac | Tumors | IGG4-RELATED DISEASE | CARDIAC & CARDIOVASCULAR SYSTEMS | CARDIAC ANGIOSARCOMA | IMAGING FINDINGS | RADIOLOGIC-PATHOLOGICAL CORRELATION | ERDHEIM-CHESTER DISEASE | MAGNETIC-RESONANCE | EPICARDIAL LIPOMA | OF-THE-LITERATURE | CONSTRICTIVE PERICARDITIS | Heart Neoplasms - pathology | Hemangioma - pathology | Mesothelioma - pathology | Hemangioma - diagnostic imaging | Humans | Heart Neoplasms - diagnostic imaging | Tomography, X-Ray Computed | Carcinoma - diagnostic imaging | Erdheim-Chester Disease - therapy | Mediastinal Cyst - therapy | Pericardium - diagnostic imaging | Lipoma - therapy | Hemangiosarcoma - therapy | Mesothelioma - therapy | Echocardiography | Paraganglioma - therapy | Lung Neoplasms - therapy | Sarcoma - pathology | Erdheim-Chester Disease - pathology | Magnetic Resonance Imaging | Mesothelioma - diagnostic imaging | Mediastinal Cyst - pathology | Lung Neoplasms - diagnostic imaging | Sarcoma - diagnostic imaging | Hemangiosarcoma - diagnostic imaging | Neoplasms, Germ Cell and Embryonal - therapy | Erdheim-Chester Disease - diagnostic imaging | Lymphoma - diagnostic imaging | Immunoglobulin G | Lung Neoplasms - pathology | Lipoma - pathology | Sarcoma - therapy | Hemangioma - therapy | Lymphoma - therapy | Pericardium - pathology | Lymphoma - pathology | Mediastinal Cyst - diagnostic imaging | Carcinoma - secondary | Sarcoma, Synovial - diagnostic imaging | Hemangiosarcoma - pathology | Paraganglioma - pathology | Sarcoma, Synovial - therapy | Heart Neoplasms - therapy | Neoplasms, Germ Cell and Embryonal - diagnostic imaging | Paraganglioma - diagnostic imaging | Breast Neoplasms - pathology | Heart Neoplasms - secondary | Autoimmune Diseases | Carcinoma - therapy | Lipoma - diagnostic imaging | Radiography, Thoracic | Sarcoma, Synovial - pathology | Neoplasms, Germ Cell and Embryonal - pathology
Journal Article
Blood, ISSN 0006-4971, 07/2017, Volume 130, Issue 2, pp. 176 - 180
Journal Article
American Journal of Surgical Pathology, ISSN 0147-5185, 10/2009, Volume 33, Issue 10, pp. 1450 - 1462
Journal Article
Human Pathology, ISSN 0046-8177, 2013, Volume 44, Issue 5, pp. 683 - 696
Journal Article
Current Opinion in Rheumatology, ISSN 1040-8711, 01/2012, Volume 24, Issue 1, pp. 53 - 59
Journal Article
Journal of Neuropathology & Experimental Neurology, ISSN 0022-3069, 12/2017, Volume 76, Issue 12, pp. 986 - 996
Journal Article