X
Search Filters
Format Format
Subjects Subjects
Subjects Subjects
X
Sort by Item Count (A-Z)
Filter by Count
familial intrahepatic cholestasis (592) 592
humans (543) 543
index medicus (326) 326
gastroenterology & hepatology (288) 288
animals (219) 219
cholestasis (212) 212
female (210) 210
male (202) 202
salt export pump (179) 179
progressive familial intrahepatic cholestasis (173) 173
liver (167) 167
cholestasis, intrahepatic - genetics (145) 145
pediatrics (144) 144
atp-binding cassette transporters - genetics (142) 142
mutation (130) 130
bile (121) 121
infant (118) 118
liver - metabolism (110) 110
child (107) 107
bile acids and salts - metabolism (106) 106
biochemistry & molecular biology (104) 104
children (103) 103
atp binding cassette subfamily b member 11 (102) 102
child, preschool (88) 88
genetic aspects (86) 86
atp-binding cassette transporters - metabolism (85) 85
farnesoid-x-receptor (83) 83
liver transplantation (82) 82
mice (82) 82
mutations (76) 76
surgery (71) 71
ursodeoxycholic acid (71) 71
p-glycoprotein (70) 70
primary biliary-cirrhosis (70) 70
adult (69) 69
adolescent (65) 65
gene (65) 65
jaundice, obstructive (65) 65
pregnancy (65) 65
liver - pathology (64) 64
atp binding cassette transporter, sub-family b - genetics (63) 63
liver-disease (63) 63
expression (62) 62
liver diseases (62) 62
pharmacology & pharmacy (62) 62
disease (59) 59
hereditary cholestasis (59) 59
adenosine triphosphatases - genetics (57) 57
bile acids (56) 56
primary sclerosing cholangitis (56) 56
infant, newborn (55) 55
rat-liver (53) 53
transplantation (53) 53
cholestasis - genetics (51) 51
biological transport (49) 49
cholestasis, intrahepatic - surgery (49) 49
bile salt export pump (46) 46
research (46) 46
hepatocytes - metabolism (45) 45
pruritus (45) 45
treatment outcome (45) 45
biliary atresia (44) 44
cholestasis, intrahepatic - metabolism (44) 44
abcb11 (43) 43
cell biology (43) 43
canalicular membrane (42) 42
gallbladder diseases (41) 41
cholestasis, intrahepatic - complications (40) 40
gastroenterology and hepatology (40) 40
phenotype (40) 40
abc transporter (39) 39
article (39) 39
cholestasis, intrahepatic - diagnosis (39) 39
deficiency (39) 39
mdr3 gene (39) 39
organic anion transporter (39) 39
cholestasis, intrahepatic - pathology (38) 38
receptors, cytoplasmic and nuclear - metabolism (38) 38
molecular sequence data (37) 37
bsep (36) 36
cholesterol (36) 36
alagille syndrome (35) 35
carrier proteins - metabolism (35) 35
cystic-fibrosis (35) 35
liver-transplantation (35) 35
risk factors (35) 35
atp8b1 (34) 34
benign recurrent intrahepatic cholestasis (34) 34
dubin-johnson-syndrome (34) 34
genetics & heredity (34) 34
nutrition & dietetics (34) 34
physiological aspects (34) 34
physiology (34) 34
transport (34) 34
analysis (33) 33
atp-binding cassette transporters - physiology (33) 33
biopsy (33) 33
cholestasis - metabolism (33) 33
disease progression (33) 33
middle aged (33) 33
more...
Library Location Library Location
Language Language
Language Language
X
Sort by Item Count (A-Z)
Filter by Count
English (776) 776
German (13) 13
French (12) 12
Spanish (10) 10
Japanese (7) 7
Polish (5) 5
Czech (3) 3
Italian (2) 2
Korean (2) 2
Turkish (2) 2
Chinese (1) 1
Slovak (1) 1
Swedish (1) 1
more...
Publication Date Publication Date
Click on a bar to filter by decade
Slide to change publication date range


Journal of Clinical and Experimental Hepatology, ISSN 0973-6883, 2013, Volume 4, Issue 1, pp. 25 - 36
Journal Article
Best Practice & Research: Clinical Gastroenterology, ISSN 1521-6918, 2010, Volume 24, Issue 5, pp. 541 - 553
Journal Article
World journal of hepatology, ISSN 1948-5182, 05/2019, Volume 11, Issue 5, pp. 450 - 463
Progressive familial intrahepatic cholestasis (PFIC) refers to a disparate group of autosomal recessive disorders that are linked by the inability to... 
Bile transport | Intrahepatic cholestasis of pregnancy | Drug induced cholestasis | Progressive familial intrahepatic cholestasis | Bile acids | Systematic Review | Cholestasis | Benign recurrent intrahepatic cholestasis
Journal Article
Journal Article
Journal Article
Journal Article
Journal of Pediatric Gastroenterology and Nutrition, ISSN 0277-2116, 11/2018, Volume 67, Issue 5, pp. 643 - 648
OBJECTIVES:In patients with progressive familial intrahepatic cholestasis (PFIC), partial external biliary diversion (PEBD), which is associated with a... 
pediatric | CHILDREN | NUTRITION & DIETETICS | bile acids | ATRESIA | neonatal cholestasis | progressive familial intrahepatic cholestasis | PEDIATRICS | HEALTH | OUTCOMES | GASTROENTEROLOGY & HEPATOLOGY | child | BILE | Development and progression | Jaundice, Obstructive | Children | Health aspects | Cholestasis | Quality of life
Journal Article
Journal of Hepatology, ISSN 0168-8278, 07/2019, Volume 71, Issue 1, pp. 153 - 162
Progressive familial intrahepatic cholestasis type 3 (PFIC3), for which there are limited therapeutic options, often leads to end-stage liver disease before... 
Adeno-associated virus | Progressive familial intrahepatic cholestasis | MDR2 | ABCB4 | AAV | PFIC type 3 | PFIC3 | Correction cholestatic phenotype | MDR3 | AAV8 | Gene therapy | HOMOZYGOUS DISRUPTION | IMMUNE-RESPONSE | HEPATOCYTES | ADENOASSOCIATED VIRUS | MDR2 P-GLYCOPROTEIN | BILIARY DIVERSION | IN-VIVO | MOUSE MODEL | DISEASE | GASTROENTEROLOGY & HEPATOLOGY | BILE
Journal Article
JOURNAL OF PEDIATRIC SURGERY, ISSN 0022-3468, 03/2018, Volume 53, Issue 3, pp. 468 - 471
Background: Partial internal biliary diversion (PIBD) is an alternative approach for the treatment of devastating pruritus in patients with progressive... 
SURGERY | LIVER-DISEASE | INTRACTABLE PRURITUS | CHILDREN | Progressive familial intrahepatic cholestasis | SURGICAL APPROACH | Long term results | Internal biliary diversion | PEDIATRICS | MUTATIONS | ILEAL EXCLUSION | Pediatric | BILE
Journal Article
Journal of Pediatrics, The, ISSN 0022-3476, 2014, Volume 164, Issue 5, pp. 1219 - 1227.e3
To examine the effects of 4-phenylbutyrate (4PB) therapy in a patient with progressive familial intrahepatic cholestasis type 2. A homozygous c.3692G>A... 
Pediatrics | TfR | Gamma-glutamyl transferase | Direct bilirubin | Aspartate aminotransaminase | Hemagglutinin | ALT | mRNA | UDCA | Alanine aminotransaminase | D-Bil | Ursodeoxycholic acid | Messenger RNA | T-Bil | cDNA | qPCR | WT | Adenosine triphosphate | G protein-coupled receptor | AST | Empty vector | BSEP | OTCD | P-gp | Quantitative polymerase chain reaction | 4PB | PFIC2 | 4-Phenylbutyrate | Wild type | Progressive familial intrahepatic cholestasis type 2 | Transferrin receptor | P-glycoprotein | Polymerase chain reaction | EV | Complementary DNA | GGT | Ornithine transcarbamylase deficiency | Glyceraldehyde-3-phosphate dehydrogenase | GPCR | HA | ATP | GAPDH | Bile salt export pump | PCR | Total bilirubin | TRANSPORT | SALT EXPORT PUMP | PEDIATRICS | MUTATIONS | EXPRESSION | DEFICIENCY | BILE | Liver Function Tests | Phenylbutyrates - therapeutic use | Cholestasis, Intrahepatic - genetics | Humans | Infant | Cholestasis, Intrahepatic - drug therapy | Genetic Markers | Homozygote | Point Mutation | ATP-Binding Cassette Transporters - genetics | ATP Binding Cassette Subfamily B Member 11 | Pruritus - drug therapy | Gastrointestinal Agents - therapeutic use | Female | Pruritus - etiology | Cholestasis, Intrahepatic - complications | Medical colleges | Care and treatment | Jaundice, Obstructive | Liver | Genetic aspects | Pruritus | Cholestasis
Journal Article
Hepatology Research, ISSN 1386-6346, 12/2018, Volume 48, Issue 13, pp. 1163 - 1171
Journal Article
Developmental period medicine, ISSN 1428-345X, 2018, Volume 22, Issue 4, pp. 385 - 389
Journal Article
Journal of Pediatric Surgery, ISSN 0022-3468, 03/2018, Volume 53, Issue 3, pp. 468 - 471
Partial internal biliary diversion (PIBD) is an alternative approach for the treatment of devastating pruritus in patients with progressive familial... 
Internal biliary diversion | Progressive familial intrahepatic cholestasis | Long term results | Pediatric
Journal Article