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Cellular and Molecular Life Sciences, ISSN 1420-682X, 6/2014, Volume 71, Issue 11, pp. 2017 - 2032
The ubiquitous distribution of lysosomes and their heterogeneous protein composition reflects the versatility of these organelles in maintaining cell... 
Life Sciences | Biochemistry, general | Protective protein/cathepsin A (PPCA) | Sialic acid | Elastin-binding protein (EBP) | Life Sciences, general | Neuraminidase 1 (NEU1) | Lysosomal exocytosis | β-Galactosidase (β-GAL) | Biomedicine general | Cell Biology | CATHEPSIN-A | CHAPERONE-MEDIATED AUTOPHAGY | BIOCHEMISTRY & MOLECULAR BIOLOGY | PLASMA-MEMBRANE | CELL BIOLOGY | beta-Galactosidase (beta-GAL) | HUMAN PROTECTIVE PROTEIN | ACID BETA-GALACTOSIDASE | GM1 GANGLIOSIDOSIS | MOUSE MODEL | ENDOPLASMIC-RETICULUM | ENZYME REPLACEMENT THERAPY | MEMBRANE-ASSOCIATED SIALIDASE | Lysosomal Storage Diseases - enzymology | Humans | Lysosomes - genetics | Lysosomes - enzymology | Multienzyme Complexes - metabolism | Neuraminidase - genetics | Gangliosidosis, GM1 - genetics | Cathepsin A - genetics | beta-Galactosidase - metabolism | Cathepsin A - metabolism | Lysosomes - pathology | Gangliosidosis, GM1 - enzymology | Disease Models, Animal | Mucolipidoses - enzymology | Signal Transduction | Gene Expression Regulation | Lysosomal Storage Diseases - genetics | Neuraminidase - metabolism | Gangliosidosis, GM1 - pathology | Mucolipidoses - genetics | Multienzyme Complexes - genetics | Lysosomal Storage Diseases - pathology | Mice, Knockout | Mucolipidoses - pathology | Animals | Mice | beta-Galactosidase - genetics | Enzymes | Hydrolases | Gangliosides | Elastin | Organic acids | Protein binding | Cellular biology | Metabolic disorders | Protective Protein | lysosomal exocytosis | Cathepsin A (PPCA) | sialic acid | elastin binding protein (EBP)
Journal Article
Journal Article
Journal Article
Journal Article
Journal of Biological Chemistry, ISSN 0021-9258, 1782, Volume 289, Issue 21, pp. 14560 - 14568
Journal Article
Journal Article
Human Mutation, ISSN 1059-7794, 07/2011, Volume 32, Issue 7, pp. 843 - 852
Journal Article