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Neurology, ISSN 0028-3878, 01/2016, Volume 86, Issue 4, pp. 351 - 359
Journal Article
Journal of Pediatric Gastroenterology and Nutrition, ISSN 0277-2116, 06/2017, Volume 64, Issue 6, pp. 864 - 868
Journal Article
Journal of Pediatric Gastroenterology and Nutrition, ISSN 0277-2116, 12/2017, Volume 65, Issue 6, pp. 613 - 620
Journal Article
RSC Advances, ISSN 2046-2069, 08/2013, Volume 3, Issue 32, pp. 13497 - 13506
Kinetically controlled and organocatalytic syn-selective transfer hydrogenation has been successfully demonstrated for the reduction of the enone functional... 
REDUCTIVE ALKYLATIONS | HUMAN DELTA-3-OXOSTEROID 5-BETA-REDUCTASE | ONE-POT COMBINATION | ASYMMETRIC TRANSFER HYDROGENATION | SUBSTRATE-SPECIFICITY | ALPHA,BETA-UNSATURATED KETONES | MULTI-CATALYSIS | CHEMICAL-SYNTHESIS | CHEMISTRY, MULTIDISCIPLINARY | MICHAEL REACTIONS | HANTZSCH ESTER
Journal Article
Journal Article
Journal of Biological Chemistry, ISSN 0021-9258, 08/2010, Volume 285, Issue 32, pp. 24529 - 24537
Bile acid deficiency is a serious syndrome in newborns that can result in death if untreated. 5 beta-Reductase deficiency is one form of bile acid deficiency... 
HUMAN DELTA-3-OXOSTEROID 5-BETA-REDUCTASE | GENE ANALYSIS | METABOLISM | CRYSTAL-STRUCTURE | BIOCHEMISTRY & MOLECULAR BIOLOGY | SUPERFAMILY | RECEPTOR | SRD5B1 AKR1D1 | BINDING | ALDO-KETO REDUCTASE | 3-ALPHA-HYDROXYSTEROID DEHYDROGENASE | Steroid | Molecular Bases of Disease | Bile Acid | Mutant | Enzyme Kinetics | Protein Stability | Enzymology | 5beta-Reduction | Aldo-keto Reductase
Journal Article
PLoS ONE, ISSN 1932-6203, 08/2016, Volume 11, Issue 8, pp. e0159203 - e0159203
Intrahepatic cholestasis of pregnancy (ICP) is a common liver disorder, mostly occurring in the third trimester. ICP is defined as an elevation of serum bile... 
CORTICOTROPIN-RELEASING HORMONE | FETAL ADRENAL-CELLS | DELTA-3-OXOSTEROID 5-BETA-REDUCTASE | SUBSTRATE-SPECIFICITY | URSODEOXYCHOLIC ACID | X RECEPTOR | POTENTIAL BIOMARKERS | SALT EXPORT PUMP | MULTIDISCIPLINARY SCIENCES | PROGESTERONE METABOLITES | BILE-ACIDS | Pregnancy Complications - pathology | Gas Chromatography-Mass Spectrometry | Area Under Curve | Humans | Alanine Transaminase - blood | Hydrocortisone - chemistry | Radioimmunoassay | Steroids - metabolism | Adult | Female | Pregnancy Complications - metabolism | Bile Acids and Salts - analysis | Hydrocortisone - blood | Steroids - blood | 17-alpha-Hydroxyprogesterone - chemistry | Steroids - chemistry | Liver Function Tests | Cholestasis, Intrahepatic - pathology | 17-alpha-Hydroxyprogesterone - blood | Pregnancy Complications - diagnosis | 17-alpha-Hydroxypregnenolone - blood | Gestational Age | Pregnancy | Cholestasis, Intrahepatic - metabolism | Aspartate Aminotransferases - blood | Cholestasis, Intrahepatic - diagnosis | ROC Curve | 17-alpha-Hydroxypregnenolone - chemistry | Dorsal Raphe Nucleus | Jaundice, Obstructive | Pregnant women | Drug metabolism | Physiological aspects | Development and progression | Genetic aspects | Research | Cholestasis | Liver | Pruritus | Bilirubin | Hydrocortisone | Metabolites | Rodents | Diols | Evaluation | Sensitivity analysis | Bile acids | Liver diseases | Secretion | Fetuses | Data processing | Regression analysis | Metabolism | Patients | Sensitivity | Acids | Steroidogenesis | Sulfate | Steroid hormones | Steroids | Bile | Index Medicus
Journal Article
Orphanet Journal of Rare Diseases, ISSN 1750-1172, 10/2018, Volume 13, Issue 1, pp. 190 - 190
Journal Article
Journal of Pediatrics, The, ISSN 0022-3476, 2015, Volume 166, Issue 1, pp. 66 - 73
Journal Article
Gastroenterology, ISSN 0016-5085, 2009, Volume 137, Issue 4, pp. 1310 - 1320.e3
Journal Article
Journal Article