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Brain, ISSN 0006-8950, 02/2015, Volume 138, Issue 2, pp. 336 - 355
Journal Article
Human Molecular Genetics, ISSN 0964-6906, 1/2008, Volume 17, Issue 1, pp. 119 - 129
Journal Article
PLoS ONE, ISSN 1932-6203, 04/2012, Volume 7, Issue 4, p. e35787
Mucopolysaccharide diseases (MPS) are caused by deficiency of glycosaminoglycan (GAG) degrading enzymes, leading to GAG accumulation. Neurodegenerative MPS... 
TARGETED DISRUPTION | MICROGLIAL ACTIVATION | SANFILIPPO-SYNDROME | DISEASE | BIOLOGY | SYNDROME TYPE-B | MICE | HEPARAN-SULFATE PROTEOGLYCANS | LYSOSOMAL STORAGE DISORDERS | ALPHA-L-IDURONIDASE | BRAIN | Immunohistochemistry | Neurons - pathology | Mucopolysaccharidosis III - pathology | Male | Parietal Lobe - metabolism | Heparitin Sulfate - metabolism | Somatosensory Cortex - pathology | Lysosomes - metabolism | Homer Scaffolding Proteins | Mucopolysaccharidosis III - metabolism | Female | Lysosomes - pathology | Neurons - metabolism | G(M2) Ganglioside - biosynthesis | Disease Models, Animal | Glycosaminoglycans - biosynthesis | Mucopolysaccharidosis I - metabolism | Mucopolysaccharidosis I - pathology | Carrier Proteins - biosynthesis | Disease Progression | Parietal Lobe - pathology | Animals | Vesicle-Associated Membrane Protein 2 - biosynthesis | Mice | Cytokines - biosynthesis | Somatosensory Cortex - metabolism | Enzymes | Brain | Neurons | Analysis | Models | Gangliosides | Animal models | Gangliosidosis | Transplants & implants | Disease | Neuropathology | Genes | Cognitive ability | Ganglioside GM2 | Schizophrenia | Cortex (somatosensory) | Mucopolysaccharidosis | Cortex (motor) | Proteins | Blood-brain barrier | Neurodegeneration | Cortex (parietal) | Rodents | Fibroblasts | Bone marrow | Growth factors | Genotypes | Heparan sulfate | Synaptophysin | Inflammation | Electron microscopy | Sulfation | Membrane proteins | Pathology | Axons | Gliosis | Hospitals | Transmission electron microscopy | Acids | Life span | Cell number | Stem cells | Monocyte chemoattractant protein 1
Journal Article
Journal Article
Proceedings of the National Academy of Sciences of the United States of America, ISSN 0027-8424, 10/2014, Volume 111, Issue 41, pp. 14870 - 14875
Journal Article
International Journal of Molecular Sciences, ISSN 1661-6596, 12/2016, Volume 17, Issue 12, pp. 2004 - 2004
Journal Article
Gene Therapy, ISSN 0969-7128, 09/2013, Volume 20, Issue 9, pp. 913 - 921
Journal Article