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Biochimica et biophysica acta. Molecular cell research, ISSN 0167-4889, 2009, Volume 1793, Issue 4, pp. 697 - 709
Animal model | Lysosomal storage disease | Neurodegeneration | NCL | Lysosome | Biochemistry & Molecular Biology | Life Sciences & Biomedicine | Science & Technology | Cell Biology | Animals | Membrane Proteins - genetics | Humans | Membrane Proteins - metabolism | Neuronal Ceroid-Lipofuscinoses - classification | Neuronal Ceroid-Lipofuscinoses - pathology | Disease Models, Animal | Neurons | Analysis | Genomics | Dementia | Membrane proteins
Journal Article
Biochimica et biophysica acta. Molecular basis of disease, ISSN 0925-4439, 09/2020, Volume 1866, Issue 9, pp. 165570 - 165570
Lysosomal storage disorders | Synaptopathy | Pathogenesis | Neurodegeneration | Glial dysfunction | Neuronal ceroid lipofuscinoses | Biochemistry & Molecular Biology | Biophysics | Life Sciences & Biomedicine | Science & Technology | Cell Biology | Membrane Proteins - genetics | Humans | Neuronal Ceroid-Lipofuscinoses - metabolism | Transcription Factors - genetics | Neuronal Ceroid-Lipofuscinoses - pathology | Transcription Factors - metabolism | Animals | Lysosomes - metabolism | Neuronal Ceroid-Lipofuscinoses - genetics | Lysosomes - pathology | Membrane Proteins - metabolism | Mutation | Disease Models, Animal | Index Medicus
Journal Article
Biochimica et biophysica acta. Molecular basis of disease, ISSN 0925-4439, 11/2013, Volume 1832, Issue 11, pp. 1795 - 1800
Neuronal ceroid-lipofuscinosis | History | Neurodegeneration | Ageing | Batten disease | Molecular genetic classification | Biochemistry & Molecular Biology | Biophysics | Life Sciences & Biomedicine | Science & Technology | Cell Biology | History, 19th Century | Neuronal Ceroid-Lipofuscinoses - genetics | Neuronal Ceroid-Lipofuscinoses - history | History, 20th Century | Humans | Neuronal Ceroid-Lipofuscinoses - pathology | Genetic research | Nervous system diseases | International cooperation | Neurons
Journal Article
Journal of neuropathology and experimental neurology, ISSN 0022-3069, 01/2003, Volume 62, Issue 1, pp. 1 - 13
Pathology | Neuronal ceroid-lipofuscinosis | Pathogenesis | Classification | Cell biology | Genetics | Batten disease | Errors of metabolism | Biological and medical sciences | Metabolic diseases | Medical sciences | Lipids (lysosomal enzyme disorders, storage diseases) | Neurons - pathology | Animals | Neuronal Ceroid-Lipofuscinoses - genetics | Animals, Genetically Modified - genetics | Humans | Brain - pathology | Neuronal Ceroid-Lipofuscinoses - classification | Neuronal Ceroid-Lipofuscinoses - pathology | Disease Models, Animal | Index Medicus
Journal Article
Developmental disabilities research reviews, ISSN 1940-5510, 06/2013, Volume 17, Issue 3, pp. 254 - 259
CLN1‐10 | apoptosis | autophagy | neuronal ceroid‐lipofuscinoses | neuronal death | batten disease | Neuronal death | CLN1-10 | Autophagy | Batten disease | Neuronal ceroid-lipofuscinoses | Apoptosis | Pediatrics | Neurosciences | Clinical Neurology | Life Sciences & Biomedicine | Neurosciences & Neurology | Psychiatry | Science & Technology | Neurological Impairments | Therapy | Genetics | Genetic Disorders | Symptoms (Individual Disorders) | Serine Proteases - metabolism | Dipeptidyl-Peptidases and Tripeptidyl-Peptidases - metabolism | Phenotype | Animals | Neuronal Ceroid-Lipofuscinoses - genetics | Humans | Neuronal Ceroid-Lipofuscinoses - metabolism | Thiolester Hydrolases - metabolism | Neuronal Ceroid-Lipofuscinoses - diagnosis | Aminopeptidases - metabolism | Neuronal Ceroid-Lipofuscinoses - pathology | Neurons | Nervous system diseases | Index Medicus
Journal Article
Biochemical and biophysical research communications, ISSN 0006-291X, 05/2020, Volume 525, Issue 4, pp. 883 - 888
Kufs | NCL | CLN6 | Biochemistry & Molecular Biology | Biophysics | Life Sciences & Biomedicine | Science & Technology | Neuronal Ceroid-Lipofuscinoses - genetics | Membrane Proteins - genetics | Humans | Membrane Proteins - metabolism | HeLa Cells | Mutation | Neuronal Ceroid-Lipofuscinoses - pathology | Amino Acid Substitution | Neurons | Analysis | Index Medicus
Journal Article