The Lancet, ISSN 0140-6736, 2005, Volume 366, Issue 9486, pp. 665 - 675
Phaeochromocytomas are rare neuroendocrine tumours with a highly variable clinical presentation but most commonly presenting with episodes of headaches,...
MEDICINE, GENERAL & INTERNAL | POSITRON-EMISSION-TOMOGRAPHY | ADRENAL-SPARING SURGERY | LAPAROSCOPIC ADRENALECTOMY | HEREDITARY PHEOCHROMOCYTOMA | EXTRAADRENAL PHEOCHROMOCYTOMA | MALIGNANT PHEOCHROMOCYTOMA | HIPPEL-LINDAU-DISEASE | CHROMOGRANIN-A | ENDOCRINE NEOPLASIA TYPE-2 | PLASMA METANEPHRINES | Pheochromocytoma - genetics | Pheochromocytoma - diagnosis | Pheochromocytoma - therapy | Humans | Causes of | Care and treatment | Pheochromocytoma | Diagnosis | Risk factors | Pathology | Adrenal glands | Medical treatment | Surgery | Diagnostic tests | Tumors
MEDICINE, GENERAL & INTERNAL | POSITRON-EMISSION-TOMOGRAPHY | ADRENAL-SPARING SURGERY | LAPAROSCOPIC ADRENALECTOMY | HEREDITARY PHEOCHROMOCYTOMA | EXTRAADRENAL PHEOCHROMOCYTOMA | MALIGNANT PHEOCHROMOCYTOMA | HIPPEL-LINDAU-DISEASE | CHROMOGRANIN-A | ENDOCRINE NEOPLASIA TYPE-2 | PLASMA METANEPHRINES | Pheochromocytoma - genetics | Pheochromocytoma - diagnosis | Pheochromocytoma - therapy | Humans | Causes of | Care and treatment | Pheochromocytoma | Diagnosis | Risk factors | Pathology | Adrenal glands | Medical treatment | Surgery | Diagnostic tests | Tumors
Journal Article
Pancreas, ISSN 0885-3177, 08/2010, Volume 39, Issue 6, pp. 775 - 783
Pheochromocytomas, intra-adrenal paraganglioma, and extra-adrenal sympathetic and parasympathetic paragangliomas are neuroendocrine tumors derived from adrenal...
medullary thyroid cancer | pheochromocytoma | neuroendocrine tumors | paraganglioma | LYMPH-NODE DISSECTION | MALIGNANT PHEOCHROMOCYTOMAS | METASTATIC PHEOCHROMOCYTOMA | GENOTYPE-PHENOTYPE CORRELATIONS | I-123 METAIODOBENZYLGUANIDINE | ENDOCRINE NEOPLASIA TYPE-2 | BIOCHEMICAL-DIAGNOSIS | POSITRON-EMISSION-TOMOGRAPHY | FUNCTIONAL PARAGANGLIOMA | LOCALIZING PHEOCHROMOCYTOMAS | GASTROENTEROLOGY & HEPATOLOGY | Thyroid Neoplasms - therapy | Thyroid Neoplasms - diagnosis | Paraganglioma - therapy | Pheochromocytoma - diagnosis | Humans | Neuroendocrine Tumors - diagnosis | Neuroendocrine Tumors - therapy | Paraganglioma - diagnosis | Pheochromocytoma - therapy
medullary thyroid cancer | pheochromocytoma | neuroendocrine tumors | paraganglioma | LYMPH-NODE DISSECTION | MALIGNANT PHEOCHROMOCYTOMAS | METASTATIC PHEOCHROMOCYTOMA | GENOTYPE-PHENOTYPE CORRELATIONS | I-123 METAIODOBENZYLGUANIDINE | ENDOCRINE NEOPLASIA TYPE-2 | BIOCHEMICAL-DIAGNOSIS | POSITRON-EMISSION-TOMOGRAPHY | FUNCTIONAL PARAGANGLIOMA | LOCALIZING PHEOCHROMOCYTOMAS | GASTROENTEROLOGY & HEPATOLOGY | Thyroid Neoplasms - therapy | Thyroid Neoplasms - diagnosis | Paraganglioma - therapy | Pheochromocytoma - diagnosis | Humans | Neuroendocrine Tumors - diagnosis | Neuroendocrine Tumors - therapy | Paraganglioma - diagnosis | Pheochromocytoma - therapy
Journal Article
Nature Reviews Endocrinology, ISSN 1759-5029, 02/2015, Volume 11, Issue 2, pp. 101 - 111
Paragangliomas and phaeochromocytomas are neuroendocrine tumours whose pathogenesis and progression are very strongly influenced by genetics. A germline...
MITOCHONDRIAL COMPLEX II | MALIGNANT PHEOCHROMOCYTOMAS | SUCCINATE-DEHYDROGENASE | POSITRON-EMISSION-TOMOGRAPHY | HIPPEL-LINDAU DISEASE | SPORADIC PHEOCHROMOCYTOMAS | ENDOCRINOLOGY & METABOLISM | TUMOR-SUPPRESSOR GENE | GERMLINE MUTATIONS | SDH MUTATIONS | METASTATIC PHEOCHROMOCYTOMAS | Neuroendocrine Tumors - pathology | Paraganglioma - pathology | Paraganglioma - genetics | Humans | Pheochromocytoma - pathology | Pheochromocytoma - genetics | Adrenal Gland Neoplasms - genetics | Adrenal Gland Neoplasms - pathology | Precision Medicine - methods | Neuroendocrine Tumors - genetics | Oncology, Experimental | Research | Cancer
MITOCHONDRIAL COMPLEX II | MALIGNANT PHEOCHROMOCYTOMAS | SUCCINATE-DEHYDROGENASE | POSITRON-EMISSION-TOMOGRAPHY | HIPPEL-LINDAU DISEASE | SPORADIC PHEOCHROMOCYTOMAS | ENDOCRINOLOGY & METABOLISM | TUMOR-SUPPRESSOR GENE | GERMLINE MUTATIONS | SDH MUTATIONS | METASTATIC PHEOCHROMOCYTOMAS | Neuroendocrine Tumors - pathology | Paraganglioma - pathology | Paraganglioma - genetics | Humans | Pheochromocytoma - pathology | Pheochromocytoma - genetics | Adrenal Gland Neoplasms - genetics | Adrenal Gland Neoplasms - pathology | Precision Medicine - methods | Neuroendocrine Tumors - genetics | Oncology, Experimental | Research | Cancer
Journal Article
The Journal of Clinical Endocrinology & Metabolism, ISSN 0021-972X, 05/2010, Volume 95, Issue 5, pp. 2023 - 2037
Context: Pheochromocytomas and paragangliomas (PHEO/PGL) are neuroendocrine tumors that arise from sympathetic and parasympathetic paraganglia. Diagnosed...
METAIODOBENZYLGUANIDINE MIBG SCINTIGRAPHY | SUCCINATE-DEHYDROGENASE | MALIGNANT PHEOCHROMOCYTOMA | SPORADIC PHEOCHROMOCYTOMAS | NECK PARAGANGLIOMAS | MEDULLARY-THYROID CANCER | HIPPEL-LINDAU-DISEASE | ENDOCRINOLOGY & METABOLISM | MULTIPLE ENDOCRINE NEOPLASIA | SURGICAL-MANAGEMENT | CHROMOGRANIN-A | Paraganglioma - therapy | Paraganglioma - genetics | Pheochromocytoma - diagnosis | Pheochromocytoma - etiology | Humans | Paraganglioma - drug therapy | Mutation, Missense | Genetic Counseling | Radiography | Paraganglioma - diagnostic imaging | Paraganglioma - etiology | Pheochromocytoma - genetics | Von Hippel-Lindau Tumor Suppressor Protein - genetics | Pheochromocytoma - diagnostic imaging | Child | Pheochromocytoma - therapy | Dopamine - metabolism
METAIODOBENZYLGUANIDINE MIBG SCINTIGRAPHY | SUCCINATE-DEHYDROGENASE | MALIGNANT PHEOCHROMOCYTOMA | SPORADIC PHEOCHROMOCYTOMAS | NECK PARAGANGLIOMAS | MEDULLARY-THYROID CANCER | HIPPEL-LINDAU-DISEASE | ENDOCRINOLOGY & METABOLISM | MULTIPLE ENDOCRINE NEOPLASIA | SURGICAL-MANAGEMENT | CHROMOGRANIN-A | Paraganglioma - therapy | Paraganglioma - genetics | Pheochromocytoma - diagnosis | Pheochromocytoma - etiology | Humans | Paraganglioma - drug therapy | Mutation, Missense | Genetic Counseling | Radiography | Paraganglioma - diagnostic imaging | Paraganglioma - etiology | Pheochromocytoma - genetics | Von Hippel-Lindau Tumor Suppressor Protein - genetics | Pheochromocytoma - diagnostic imaging | Child | Pheochromocytoma - therapy | Dopamine - metabolism
Journal Article
Cancer, ISSN 0008-543X, 06/2012, Volume 118, Issue 11, pp. 2804 - 2812
BACKGROUND: The objective of this study was to evaluate the clinical benefits of systemic chemotherapy for patients with metastatic pheochromocytomas or...
chemotherapy | clinical benefits | metastatic pheochromocytoma and paraganglioma | survival | MANAGEMENT | CYCLOPHOSPHAMIDE | TUMOR RESPONSE | I-131-MIBG | BIOCHEMICAL-DIAGNOSIS | ONCOLOGY | MALIGNANT PHEOCHROMOCYTOMA | DISEASE | VINCRISTINE | INHIBITOR SUNITINIB | Blood Pressure | Adrenal Gland Neoplasms - drug therapy | Paraganglioma, Extra-Adrenal - pathology | Humans | Middle Aged | Male | Paraganglioma, Extra-Adrenal - physiopathology | Pheochromocytoma - mortality | Pheochromocytoma - physiopathology | Adrenal Gland Neoplasms - physiopathology | Pheochromocytoma - drug therapy | Adrenal Gland Neoplasms - mortality | Neoplasm Metastasis | Antineoplastic Combined Chemotherapy Protocols - therapeutic use | Paraganglioma, Extra-Adrenal - drug therapy | Aged, 80 and over | Pheochromocytoma - pathology | Adult | Female | Paraganglioma, Extra-Adrenal - mortality | Adrenal Gland Neoplasms - pathology | Chromaffin cells | Chemotherapy | Care and treatment | Pheochromocytoma | Patient outcomes | Research | Diagnosis | Health aspects | Cancer | metastatic pheochromocytoma | paraganglioma
chemotherapy | clinical benefits | metastatic pheochromocytoma and paraganglioma | survival | MANAGEMENT | CYCLOPHOSPHAMIDE | TUMOR RESPONSE | I-131-MIBG | BIOCHEMICAL-DIAGNOSIS | ONCOLOGY | MALIGNANT PHEOCHROMOCYTOMA | DISEASE | VINCRISTINE | INHIBITOR SUNITINIB | Blood Pressure | Adrenal Gland Neoplasms - drug therapy | Paraganglioma, Extra-Adrenal - pathology | Humans | Middle Aged | Male | Paraganglioma, Extra-Adrenal - physiopathology | Pheochromocytoma - mortality | Pheochromocytoma - physiopathology | Adrenal Gland Neoplasms - physiopathology | Pheochromocytoma - drug therapy | Adrenal Gland Neoplasms - mortality | Neoplasm Metastasis | Antineoplastic Combined Chemotherapy Protocols - therapeutic use | Paraganglioma, Extra-Adrenal - drug therapy | Aged, 80 and over | Pheochromocytoma - pathology | Adult | Female | Paraganglioma, Extra-Adrenal - mortality | Adrenal Gland Neoplasms - pathology | Chromaffin cells | Chemotherapy | Care and treatment | Pheochromocytoma | Patient outcomes | Research | Diagnosis | Health aspects | Cancer | metastatic pheochromocytoma | paraganglioma
Journal Article
2006, Volume 1073.
Conference Proceeding
8.
Full Text
Current and Future Treatments for Malignant Pheochromocytoma and Sympathetic Paraganglioma
Current Oncology Reports, ISSN 1523-3790, 8/2013, Volume 15, Issue 4, pp. 356 - 371
Pheochromocytomas (PHs) and sympathetic paragangliomas (SPGs) are rare neuroendocrine tumors. Approximately 17 % of these tumors are malignant, but because no...
Chemotherapy | Medicine & Public Health | Surgery | Oncology | Malignant pheochromocytoma | Malignant paraganglioma | Metaiodobenzylguanidine | Molecular targeted therapies | METASTATIC PHEOCHROMOCYTOMA | NEUROENDOCRINE TUMORS | CARNEY-STRATAKIS-SYNDROME | B GENE-MUTATIONS | LABELED DOPAMINE CONCENTRATION | SPORADIC PHEOCHROMOCYTOMA | POSITRON-EMISSION-TOMOGRAPHY | ONCOLOGY | ADRENAL-MEDULLA | COMBINATION CHEMOTHERAPY | APPARENTLY BENIGN PHEOCHROMOCYTOMA | Succinate Dehydrogenase - genetics | Paraganglioma - therapy | Paraganglioma - genetics | Pheochromocytoma - diagnosis | Humans | Pheochromocytoma - genetics | Antineoplastic Agents - therapeutic use | Combined Modality Therapy | Paraganglioma - diagnosis | Pheochromocytoma - therapy | Molecular Targeted Therapy - methods | Radiopharmaceuticals - therapeutic use | Care and treatment | Pheochromocytoma | PET imaging | Gene mutations | Health aspects | Tumors | Cancer
Chemotherapy | Medicine & Public Health | Surgery | Oncology | Malignant pheochromocytoma | Malignant paraganglioma | Metaiodobenzylguanidine | Molecular targeted therapies | METASTATIC PHEOCHROMOCYTOMA | NEUROENDOCRINE TUMORS | CARNEY-STRATAKIS-SYNDROME | B GENE-MUTATIONS | LABELED DOPAMINE CONCENTRATION | SPORADIC PHEOCHROMOCYTOMA | POSITRON-EMISSION-TOMOGRAPHY | ONCOLOGY | ADRENAL-MEDULLA | COMBINATION CHEMOTHERAPY | APPARENTLY BENIGN PHEOCHROMOCYTOMA | Succinate Dehydrogenase - genetics | Paraganglioma - therapy | Paraganglioma - genetics | Pheochromocytoma - diagnosis | Humans | Pheochromocytoma - genetics | Antineoplastic Agents - therapeutic use | Combined Modality Therapy | Paraganglioma - diagnosis | Pheochromocytoma - therapy | Molecular Targeted Therapy - methods | Radiopharmaceuticals - therapeutic use | Care and treatment | Pheochromocytoma | PET imaging | Gene mutations | Health aspects | Tumors | Cancer
Journal Article
The Oncologist, ISSN 1083-7159, 07/2008, Volume 13, Issue 7, pp. 779 - 793
Learning Objectives After completing this course, the reader should be able to: Use current practice methods in the diagnosis of pheochromocytomas. Employ...
Familial pheochromocytoma | Pheochromocytoma | Management | Adrenal gland | CLONIDINE SUPPRESSION TEST | HIPPEL-LINDAU-SYNDROME | pheochromocytoma | ENDOCRINE NEOPLASIA TYPE-2 | CALCIUM-CHANNEL BLOCKERS | BIOCHEMICAL-DIAGNOSIS | PREOPERATIVE MANAGEMENT | POSITRON-EMISSION-TOMOGRAPHY | ONCOLOGY | management | MALIGNANT PHEOCHROMOCYTOMA | GERMLINE MUTATIONS | adrenal gland | LOCALIZING PHEOCHROMOCYTOMAS | familial pheochromocytoma | Adrenal Gland Neoplasms - diagnosis | Genetic Predisposition to Disease | Neoplasm Metastasis - prevention & control | Pheochromocytoma - diagnosis | Humans | Pheochromocytoma - genetics | Chemotherapy, Adjuvant | Radiotherapy, Adjuvant | Adrenal Gland Neoplasms - genetics | Adrenal Glands - surgery | Pheochromocytoma - therapy | Adrenal Gland Neoplasms - therapy
Familial pheochromocytoma | Pheochromocytoma | Management | Adrenal gland | CLONIDINE SUPPRESSION TEST | HIPPEL-LINDAU-SYNDROME | pheochromocytoma | ENDOCRINE NEOPLASIA TYPE-2 | CALCIUM-CHANNEL BLOCKERS | BIOCHEMICAL-DIAGNOSIS | PREOPERATIVE MANAGEMENT | POSITRON-EMISSION-TOMOGRAPHY | ONCOLOGY | management | MALIGNANT PHEOCHROMOCYTOMA | GERMLINE MUTATIONS | adrenal gland | LOCALIZING PHEOCHROMOCYTOMAS | familial pheochromocytoma | Adrenal Gland Neoplasms - diagnosis | Genetic Predisposition to Disease | Neoplasm Metastasis - prevention & control | Pheochromocytoma - diagnosis | Humans | Pheochromocytoma - genetics | Chemotherapy, Adjuvant | Radiotherapy, Adjuvant | Adrenal Gland Neoplasms - genetics | Adrenal Glands - surgery | Pheochromocytoma - therapy | Adrenal Gland Neoplasms - therapy
Journal Article
The New England Journal of Medicine, ISSN 0028-4793, 08/2019, Volume 381, Issue 6, pp. 552 - 565
Pheochromocytoma and paraganglioma are related tumors that differ mainly in location; pheochromocytomas are adrenal, and paragangliomas can be anywhere else....
MALIGNANT PHEOCHROMOCYTOMAS | MEDICINE, GENERAL & INTERNAL | SUCCINATE-DEHYDROGENASE | ADRENAL-SPARING SURGERY | LAPAROSCOPIC ADRENALECTOMY | GERM-LINE MUTATIONS | HIF2A MUTATIONS | RETROPERITONEAL PARAGANGLIOMAS | ENDOCRINE NEOPLASIA TYPE-2 | RENAL-CELL CARCINOMA | FAMILIAL PHEOCHROMOCYTOMA | Adrenal Gland Neoplasms - surgery | Pheochromocytoma - history | Diagnosis, Differential | History, 21st Century | Pheochromocytoma - diagnosis | History, 20th Century | Humans | Paraganglioma, Extra-Adrenal - surgery | Male | Adrenal Gland Neoplasms - diagnosis | Paraganglioma, Extra-Adrenal - genetics | Female | History, 19th Century | Pheochromocytoma - genetics | Adrenal Gland Neoplasms - history | Paraganglioma, Extra-Adrenal - diagnosis | Pheochromocytoma - surgery | Adrenal Gland Neoplasms - genetics | Hypertension | Nuclear magnetic resonance--NMR | Pheochromocytoma | Paraganglioma | Metastasis | Preventive medicine | Patients | Prevention | Psychotropic drugs | Pregnancy | Genetic counseling | Surveillance | Mutation | Localization | Tumors
MALIGNANT PHEOCHROMOCYTOMAS | MEDICINE, GENERAL & INTERNAL | SUCCINATE-DEHYDROGENASE | ADRENAL-SPARING SURGERY | LAPAROSCOPIC ADRENALECTOMY | GERM-LINE MUTATIONS | HIF2A MUTATIONS | RETROPERITONEAL PARAGANGLIOMAS | ENDOCRINE NEOPLASIA TYPE-2 | RENAL-CELL CARCINOMA | FAMILIAL PHEOCHROMOCYTOMA | Adrenal Gland Neoplasms - surgery | Pheochromocytoma - history | Diagnosis, Differential | History, 21st Century | Pheochromocytoma - diagnosis | History, 20th Century | Humans | Paraganglioma, Extra-Adrenal - surgery | Male | Adrenal Gland Neoplasms - diagnosis | Paraganglioma, Extra-Adrenal - genetics | Female | History, 19th Century | Pheochromocytoma - genetics | Adrenal Gland Neoplasms - history | Paraganglioma, Extra-Adrenal - diagnosis | Pheochromocytoma - surgery | Adrenal Gland Neoplasms - genetics | Hypertension | Nuclear magnetic resonance--NMR | Pheochromocytoma | Paraganglioma | Metastasis | Preventive medicine | Patients | Prevention | Psychotropic drugs | Pregnancy | Genetic counseling | Surveillance | Mutation | Localization | Tumors
Journal Article
CLINICAL CANCER RESEARCH, ISSN 1078-0432, 09/2015, Volume 21, Issue 17, pp. 3888 - 3895
Purpose: Patients with succinate dehydrogenase subunit B (SDHB) mutation-related pheochromocytoma/paraganglioma (PHEO/PGL) are at a higher risk for metastatic...
RADIOLABELED SOMATOSTATIN ANALOG | MALIGNANT PHEOCHROMOCYTOMAS | POSITRON-EMISSION-TOMOGRAPHY | NEUROENDOCRINE TUMORS | THERAPY | ONCOLOGY | GERMLINE MUTATIONS | HIGH-FREQUENCY | I-123-MIBG SPECT | FOLLOW-UP | GA-68-DOTATATE PET/CT |
RADIOLABELED SOMATOSTATIN ANALOG | MALIGNANT PHEOCHROMOCYTOMAS | POSITRON-EMISSION-TOMOGRAPHY | NEUROENDOCRINE TUMORS | THERAPY | ONCOLOGY | GERMLINE MUTATIONS | HIGH-FREQUENCY | I-123-MIBG SPECT | FOLLOW-UP | GA-68-DOTATATE PET/CT |