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Experimental & molecular medicine, ISSN 1226-3613, 2015, Volume 47, Issue 3, pp. e147 - e147
Biochemistry & Molecular Biology | Life Sciences & Biomedicine | Medicine, Research & Experimental | Science & Technology | Research & Experimental Medicine | Proteostasis Deficiencies - metabolism | Humans | Ubiquitin - metabolism | tau Proteins - metabolism | Parkinson Disease - drug therapy | Molecular Targeted Therapy | Neurodegenerative Diseases - drug therapy | Amyotrophic Lateral Sclerosis - drug therapy | Autophagy - drug effects | DNA-Binding Proteins - metabolism | PrPSc Proteins - metabolism | Lysosomes - metabolism | Proteolysis | Amyloid beta-Peptides - metabolism | Parkinson Disease - metabolism | Huntington Disease - drug therapy | Superoxide Dismutase - metabolism | Prion Diseases - drug therapy | Alzheimer Disease - drug therapy | Neurodegenerative Diseases - metabolism | Huntington Disease - metabolism | Nerve Tissue Proteins - genetics | Nerve Tissue Proteins - metabolism | Huntingtin Protein | Animals | Alzheimer Disease - metabolism | Amyotrophic Lateral Sclerosis - metabolism | Huntington Disease - genetics | Mutation | Proteasome Endopeptidase Complex - metabolism | alpha-Synuclein - metabolism | Prion Diseases - metabolism | Index Medicus | Review
Journal Article
Nature (London), ISSN 0028-0836, 05/2012, Volume 485, Issue 7399, pp. 507 - 511
Science & Technology - Other Topics | Multidisciplinary Sciences | Science & Technology | Neurology | Organic mental disorders. Neuropsychology | Psychology. Psychoanalysis. Psychiatry | Adult and adolescent clinical studies | Degenerative and inherited degenerative diseases of the nervous system. Leukodystrophies. Prion diseases | Psychopathology. Psychiatry | Biological and medical sciences | Medical sciences | Neurons - pathology | Neuroprotective Agents | Phosphorylation | Prions - genetics | Eukaryotic Initiation Factor-2 - chemistry | Neurodegenerative Diseases - etiology | PrPSc Proteins - analysis | Synapses - pathology | Thiourea - pharmacology | Phosphoproteins - metabolism | Repressor Proteins - analysis | PrPSc Proteins - metabolism | Synapses - metabolism | Phosphoproteins - analysis | Protein Folding - drug effects | Protein Phosphatase 1 - genetics | Eukaryotic Initiation Factor-2 - metabolism | Synaptic Transmission - drug effects | Cell Death - drug effects | PrPSc Proteins - toxicity | Neurons - drug effects | Repressor Proteins - metabolism | Prions - metabolism | Synapses - drug effects | Repressor Proteins - chemistry | Neurodegenerative Diseases - pathology | Mice, Inbred C57BL | Kaplan-Meier Estimate | Hippocampus - pathology | Prion Diseases - pathology | Neurodegenerative Diseases - metabolism | Hippocampus - cytology | Cinnamates - pharmacology | Eukaryotic Initiation Factor-2 - analysis | Hippocampus - metabolism | Protein Phosphatase 1 - metabolism | Animals | Prions - biosynthesis | Protein Biosynthesis - drug effects | Mice | Unfolded Protein Response - physiology | Thiourea - analogs & derivatives | Index Medicus
Journal Article
Laboratory animals (London), ISSN 0023-6772, 4/2013, Volume 47, Issue 2, pp. 106 - 115
Prion | Cell assay | Protein misfolding cyclic amplification (PMCA) | Prion protein | Reduction of animal bioassays | Veterinary Sciences | Life Sciences & Biomedicine | Zoology | Science & Technology | Prion Diseases - genetics | Protein Engineering - methods | Neuroglia - pathology | Humans | PrPC Proteins - chemistry | PrPSc Proteins - chemistry | PrPSc Proteins - metabolism | Cattle Diseases - metabolism | Cattle | Sensitivity and Specificity | Encephalopathy, Bovine Spongiform - metabolism | PrPC Proteins - metabolism | PrPC Proteins - genetics | Biological Assay - instrumentation | Protein Engineering - instrumentation | Cricetinae | Electrophoresis, Polyacrylamide Gel | Biological Assay - methods | Scrapie - metabolism | Blotting, Western | Protein Folding | PrPSc Proteins - genetics | Creutzfeldt-Jakob Syndrome - metabolism | Animals | Disinfection - methods | Neuroglia - metabolism | Sheep - metabolism | Prion Diseases - metabolism | Index Medicus
Journal Article
The Journal of biological chemistry, ISSN 0021-9258, 08/2009, Volume 284, Issue 34, pp. 22590 - 22600
Life Sciences & Biomedicine | Biochemistry & Molecular Biology | Science & Technology | ADAM17 Protein | Amyloid Precursor Protein Secretases - genetics | Humans | Immunoblotting | Aspartic Acid Endopeptidases - genetics | PrPSc Proteins - metabolism | Mass Spectrometry | Membrane Proteins - metabolism | PrPC Proteins - metabolism | PrPC Proteins - genetics | Recombinant Proteins - metabolism | Cell Line | Membrane Proteins - genetics | ADAM10 Protein | Recombinant Proteins - genetics | Reverse Transcriptase Polymerase Chain Reaction | PrPSc Proteins - genetics | ADAM Proteins - metabolism | Amyloid Precursor Protein Secretases - metabolism | Animals | Aspartic Acid Endopeptidases - metabolism | Cell Line, Tumor | Mice | RNA, Small Interfering | ADAM Proteins - genetics | DNA, Complementary | Index Medicus | Protein Synthesis, Post-Translational Modification, and Degradation
Journal Article
Nature communications, ISSN 2041-1723, 2013, Volume 4, Issue 1, pp. 1846 - 1846
Science & Technology - Other Topics | Multidisciplinary Sciences | Science & Technology | Humans | Male | Endosomes - metabolism | Brain - metabolism | PrPSc Proteins - metabolism | Endocytosis | Biotin - metabolism | Cell Membrane - metabolism | Membrane Proteins - metabolism | PrPC Proteins - metabolism | Cell Line | Prions - metabolism | Cricetinae | Signal Transduction | Subcellular Fractions - metabolism | Blotting, Western | Protein Transport | Insulin - metabolism | Animals | Models, Biological | Brain - pathology | Golgi Apparatus - metabolism | Receptor, Insulin - metabolism | Mice | Antibodies, Monoclonal - metabolism | Index Medicus
Journal Article
Science (American Association for the Advancement of Science), ISSN 0036-8075, 10/2003, Volume 302, Issue 5646, pp. 814 - 818
Brain | Nervous system diseases | Presenilins | Neurons | Prions | Parkinson disease | Lead | Prion diseases | Biochemistry | Alzheimers disease | Reviews and Viewpoints | Science & Technology - Other Topics | Multidisciplinary Sciences | Science & Technology | Presenilin-2 | Presenilin-1 | Amyloid beta-Protein Precursor - chemistry | Humans | PrPC Proteins - chemistry | PrPSc Proteins - chemistry | Alzheimer Disease - pathology | Brain - metabolism | PrPSc Proteins - metabolism | Aspartic Acid Endopeptidases | Amyloid Precursor Protein Secretases | Amyloid beta-Peptides - metabolism | Amyloid beta-Protein Precursor - metabolism | Membrane Proteins - metabolism | PrPC Proteins - metabolism | PrPC Proteins - genetics | Endopeptidases - metabolism | Membrane Proteins - genetics | Terminology as Topic | Prion Diseases - pathology | PrPC Proteins - classification | Protein Folding | Creutzfeldt-Jakob Syndrome - metabolism | PrPSc Proteins - classification | Animals | Membrane Proteins - chemistry | Alzheimer Disease - metabolism | Brain - pathology | Creutzfeldt-Jakob Syndrome - pathology | Amyloid beta-Peptides - chemistry | Mutation | Prion Diseases - metabolism | Index Medicus
Journal Article
The Journal of neuroscience, ISSN 0270-6474, 03/2010, Volume 30, Issue 13, pp. 4528 - 4535
Neurosciences | Neurosciences & Neurology | Life Sciences & Biomedicine | Science & Technology | Prions - metabolism | Mice, Inbred C57BL | Mice, Transgenic | Prion Diseases - pathology | Prions - chemistry | PrPSc Proteins - chemistry | Protein Folding | Alzheimer Disease - pathology | Brain - metabolism | PrPSc Proteins - metabolism | Animals | Amyloid - metabolism | Alzheimer Disease - metabolism | Amyloid beta-Peptides - metabolism | Brain - pathology | Mice | Amyloid beta-Peptides - chemistry | Prion Diseases - metabolism | Index Medicus
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Roles of endoproteolytic α‐cleavage and shedding of the prion protein in neurodegeneration
The FEBS journal, ISSN 1742-464X, 09/2013, Volume 280, Issue 18, pp. 4338 - 4347
prion disease | α‐cleavage | β‐amyloid | neurotoxic oligomers | neurodegeneration | ADAM10 | shedding | Alzheimer's disease | prion protein | α-cleavage | β-amyloid | Life Sciences & Biomedicine | Biochemistry & Molecular Biology | Science & Technology | Amyloid Precursor Protein Secretases - genetics | Prion Diseases - genetics | Humans | Alzheimer Disease - pathology | PrPSc Proteins - metabolism | Prion Diseases - enzymology | Amyloid beta-Peptides - genetics | Proteolysis | Amyloid beta-Peptides - metabolism | Membrane Proteins - metabolism | PrPC Proteins - metabolism | PrPC Proteins - genetics | Cell Line | Signal Transduction | Membrane Proteins - genetics | ADAM10 Protein | Prion Diseases - pathology | Alzheimer Disease - enzymology | Protein Folding | PrPSc Proteins - genetics | ADAM Proteins - metabolism | Amyloid Precursor Protein Secretases - metabolism | Protein Conformation | Protein Processing, Post-Translational | ADAM Proteins - genetics | Alzheimer Disease - genetics | Index Medicus
Journal Article