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Journal Article
Proceedings of the National Academy of Sciences of the United States of America, ISSN 0027-8424, 9/2000, Volume 97, Issue 20, pp. 10954 - 10959
Journal Article
Neurobiology of Disease, ISSN 0969-9961, 2015, Volume 85, pp. 174 - 186
Journal Article
Journal Article
Proceedings of the National Academy of Sciences of the United States of America, ISSN 0027-8424, 7/2006, Volume 103, Issue 27, pp. 10373 - 10378
Tay-Sachs disease is a prototypic neurodegenerative disease. Lysosomal storage of GM2 ganglioside in Tay-Sachs and the related disorder, Sandhoff disease, is... 
Nervous system diseases | Spinal cord | Genetic vectors | Neurodegenerative diseases | Mice | Gene therapy | Sandhoff disease | Gangliosides | Tay Sachs disease | Gangliosidoses | GM2 gangliosidosis | Neurodegeneration | Adeno-associated virus | LYSOSOMAL STORAGE DISEASE | BONE-MARROW-TRANSPLANTATION | MULTIDISCIPLINARY SCIENCES | neurodegeneration | adeno-associated virus | SANDHOFF-DISEASE | VIRAL VECTORS | N-BUTYLDEOXYNOJIRIMYCIN | MOUSE MODELS | BETA-HEXOSAMINIDASE ACTIVITY | CENTRAL-NERVOUS-SYSTEM | MICE | Inflammation - pathology | Tay-Sachs Disease - therapy | beta-N-Acetylhexosaminidases - metabolism | Survival Rate | Microscopy, Electron | Body Weight - genetics | Tay-Sachs Disease - genetics | Genetic Vectors - genetics | Protein Subunits - metabolism | Mice, Knockout | beta-N-Acetylhexosaminidases - deficiency | Gene Expression Regulation, Enzymologic | Inflammation - metabolism | Animals | Tay-Sachs Disease - metabolism | Glycosphingolipids - metabolism | Inflammation - genetics | Tay-Sachs Disease - pathology | Inflammation - prevention & control | beta-N-Acetylhexosaminidases - genetics | Disease Models, Animal | Genetic Therapy - methods | Protein Subunits - genetics | Tay-Sachs disease | Research | Proteins | Nervous system | Genetic disorders | Neurological disorders | Index Medicus | Biological Sciences
Journal Article
Experimental Neurology, ISSN 0014-4886, 01/2015, Volume 263, pp. 102 - 112
Journal Article
Proceedings of the National Academy of Sciences of the United States of America, ISSN 0027-8424, 5/1999, Volume 96, Issue 11, pp. 6388 - 6393
Journal Article
Neuroscience, ISSN 0306-4522, 2016, Volume 340, pp. 117 - 125
Journal Article
Journal Article