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Annals of Cardiac Anaesthesia, ISSN 0971-9784, 10/2019, Volume 22, Issue 4, p. 412
Journal Article
British Journal of Pharmacology, ISSN 0007-1188, 08/2019, Volume 176, Issue 16, p. 2945
Impaired endothelium-dependent relaxation (EDR) is a hallmark of endothelial dysfunction. A deficiency of tetrahydrobiopterin (BH.sub.4) causes endothelial NOS... 
Unsaturated fatty acids | Genes | Dihydrofolate reductase | Methotrexate | Saturated fatty acids | Sapropterin dihydrochloride | Omega-3 fatty acids | Endothelium
Journal Article
Nitric Oxide, ISSN 1089-8603, 01/2020, Volume 94, pp. 9 - 18
Endothelial nitric oxide synthase (eNOS) and oxidative stress are critical to embryonic coronary artery development. Maternal diabetes increases oxidative... 
Sapropterin | Embryonic heart development | Oxidative stress | Tetrahydrobiopterin | Coronary artery malformation | Pregestational diabetes
Journal Article
Orphanet Journal of Rare Diseases, ISSN 1750-1172, 09/2018, Volume 13, Issue 1, pp. 173 - 9
Journal Article
American Journal of Health-System Pharmacy, ISSN 1079-2082, 02/2014, Volume 71, Issue 3, p. 174
Journal Article
by Han, Xu and Yu, Jing
Journal of Hypertension, ISSN 0263-6352, 10/2018, Volume 36 Suppl 3, pp. e7 - e7
OBJECTIVES:To identify the influence of tetrahydrobiopterin (BH4) on left ventricular (LV) diastolic function and the expression of protein kinase C ε (PKC ε)... 
Heart failure | Oxidative stress | Care and treatment | Influence | Cellular signal transduction | Research | Protein kinases | Sapropterin dihydrochloride | Health aspects
Journal Article
MONATSSCHRIFT KINDERHEILKUNDE, ISSN 0026-9298, 04/2013, Volume 161, Issue 4, pp. 293 - 295
Journal Article
Human Molecular Genetics, ISSN 0964-6906, 09/2019, Volume 28, Issue 17, pp. 2885 - 2899
Abstract Sulfite oxidase (SO) is encoded by the nuclear SUOX gene and catalyzes the final step in cysteine catabolism thereby oxidizing sulfite to sulfate.... 
STRUCTURAL INSIGHTS | DOMAIN | INTRAMOLECULAR ELECTRON-TRANSFER | BIOCHEMISTRY & MOLECULAR BIOLOGY | HPLC METHOD | GENETICS & HEREDITY | MOLYBDENUM COFACTOR DEFICIENCY | SAPROPTERIN | MUTATIONS | G473D
Journal Article
Molecular Genetics and Metabolism, ISSN 1096-7192, 06/2015, Volume 115, Issue 2-3, pp. 78 - 83
Phenylketonuria (PKU) is an autosomal recessive disorder caused by deficiency of hepatic phenylalanine hydroxylase (PAH) leading to increased levels of... 
Sapropterin | Phenylketonuria | Breath test | Phenylalanine hydroxylase | 13C-phenylalanine | Stable isotopes
Journal Article
Orphanet Journal of Rare Diseases, ISSN 1750-1172, 03/2017, Volume 12, Issue 1, p. 47
Journal Article