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Biochimica et biophysica acta. Bioenergetics, ISSN 0005-2728, 08/2016, Volume 1857, Issue 8, pp. 1079 - 1085
Mitochondrial disorders | Coenzyme Q | Ubiquinone | Coenzyme Q10 deficiency | Steroid resistant nephrotic syndrome | Adenosine Triphosphate - deficiency | Electron Transport | Reactive Oxygen Species - metabolism | Saccharomyces cerevisiae - genetics | Humans | Protein Multimerization | Ubiquinone - deficiency | Mitochondrial Diseases - metabolism | Ubiquinone - metabolism | Adenosine Triphosphate - agonists | Adenosine Triphosphate - biosynthesis | Muscle Weakness - genetics | Ubiquinone - biosynthesis | Saccharomyces cerevisiae - metabolism | Mitochondria - genetics | Ataxia - drug therapy | Ubiquinone - therapeutic use | Ataxia - genetics | Ataxia - metabolism | Mitochondrial Diseases - genetics | Ataxia - physiopathology | Mitochondrial Diseases - drug therapy | Electron Transport Chain Complex Proteins - genetics | Mitochondria - metabolism | Ubiquinone - genetics | Reactive Oxygen Species - antagonists & inhibitors | Animals | Electron Transport Chain Complex Proteins - metabolism | Muscle Weakness - drug therapy | Muscle Weakness - metabolism | Muscle Weakness - physiopathology | Mutation | Mitochondrial Diseases - physiopathology | Physiological aspects | Enzymes | Phosphatases | Cytochrome b | Permeability | Quinone | Antioxidants | Genes | Kidney diseases
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Nature structural & molecular biology, ISSN 1545-9993, 06/2018, Volume 25, Issue 7, pp. 548 - 556
Protein Subunits | Mitochondria, Heart - enzymology | Models, Molecular | Phospholipids - chemistry | Ubiquinone - metabolism | NADH Dehydrogenase - ultrastructure | NADH Dehydrogenase - chemistry | NADH Dehydrogenase - metabolism | Nucleotides - metabolism | Electron Transport Complex I - metabolism | Nucleotides - chemistry | Cryoelectron Microscopy | Protein Structural Elements | Electron Transport Complex I - chemistry | Animals | Protein Structure, Quaternary | Electron Transport Complex I - ultrastructure | Mice | Enzyme Activation | Phospholipids - metabolism | Binding Sites | Ubiquinone - chemistry | Heart | Mitochondria | Usage | NADH dehydrogenase | Physiological aspects | Models | Electron microscopy | Protons | NADH-ubiquinone oxidoreductase | Phosphorylation | Animal models | Oxidoreductase | Homology | Mammals | Electron transport chain | Ubiquinone | Reperfusion | NADH | Ischemia | Oxidative phosphorylation | Rodents | Nicotinamide adenine dinucleotide | Ubiquinone oxidoreductase
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The Journal of clinical investigation, ISSN 0021-9738, 12/2013, Volume 123, Issue 12, pp. 5179 - 5189
Protein Kinases - genetics | Humans | Nephrotic Syndrome - metabolism | Molecular Sequence Data | Ubiquinone - metabolism | Nephrotic Syndrome - genetics | Nephrotic Syndrome - drug therapy | Adrenal Cortex Hormones - therapeutic use | Zebrafish - embryology | Gene Knockdown Techniques | Ubiquinone - biosynthesis | Young Adult | DNA Mutational Analysis | Conserved Sequence | Ubiquinone - therapeutic use | Protein Kinases - deficiency | Child | Drosophila Proteins - antagonists & inhibitors | Drug Resistance | Disease Models, Animal | Fibroblasts - metabolism | Amino Acid Sequence | Podocytes - metabolism | Ubiquinone - analogs & derivatives | Zebrafish Proteins - antagonists & inhibitors | Cells, Cultured | Adrenal Cortex Hormones - pharmacology | Nephrotic Syndrome - pathology | Rats | Ubiquinone - antagonists & inhibitors | Zebrafish - genetics | Sequence Homology, Amino Acid | Exome - genetics | Podocytes - ultrastructure | Sequence Alignment | Animals | Protein Kinases - physiology | Adolescent | Consanguinity | Drosophila Proteins - genetics | Mutation | Zebrafish Proteins - genetics | Mitochondria - physiology | Biosynthesis | Nephrotic syndrome | Genetic aspects | Research | Gene mutations | Index Medicus | Abridged Index Medicus
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Essays in biochemistry, ISSN 0071-1365, 07/2018, Volume 62, Issue 3, pp. 377 - 398
Mitochondrial Diseases - genetics | Ataxia - physiopathology | Ataxia - therapy | Muscle Weakness - diagnosis | Humans | Ubiquinone - analogs & derivatives | Ubiquinone - deficiency | Genotype | Structure-Activity Relationship | Ubiquinone - genetics | Ataxia - diagnosis | Muscle Weakness - genetics | Syndrome | Ubiquinone - biosynthesis | Phenotype | Ubiquinone - physiology | Mitochondrial Diseases - therapy | Muscle Weakness - physiopathology | Muscle Weakness - therapy | Mutation | Ataxia - genetics | Mitochondrial Diseases - physiopathology | Mitochondrial Diseases - diagnosis | Ubiquinone - chemistry
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Bioavailability of coenzyme Q10 supplements depends on carrier lipids and solubilization
Nutrition (Burbank, Los Angeles County, Calif.), ISSN 0899-9007, 01/2019, Volume 57, pp. 133 - 140
Human | Ubiquinol | Ubiquinone | Bioavailability | Coenzyme Q10 | Life Sciences & Biomedicine | Nutrition & Dietetics | Science & Technology | Ubiquinone - administration & dosage | Ubiquinone - pharmacokinetics | Double-Blind Method | Administration, Oral | Area Under Curve | Humans | Ubiquinone - analogs & derivatives | Solubility | Biological Availability | Lipids | Male | Drug Carriers | Cross-Over Studies | Young Adult | Capsules | Adolescent | Adult | Female | Dietary Supplements | Ubiquinone - chemistry | Antioxidants | Enzymes | Plasma | Preservatives | Physiological effects | Ascorbic acid | Statistical analysis | Dehydrogenases | Solubilization | Chromatography | Ingestion | Lipoproteins | Physiological factors | Physiology | Drug dosages | Crystal structure
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The Journal of biological chemistry, ISSN 0021-9258, 05/2020, Volume 295, Issue 18, pp. 6023 - 6042
Life Sciences & Biomedicine | Biochemistry & Molecular Biology | Science & Technology | Gene Expression Regulation, Fungal | Saccharomyces cerevisiae - genetics | Humans | Ubiquinone - analogs & derivatives | Ubiquinone - deficiency | Ubiquinone - metabolism | Mitochondria - metabolism | Ubiquinone - genetics | Saccharomyces cerevisiae Proteins - genetics | Gene Knockout Techniques | Protein Transport | Ubiquinone - biosynthesis | Saccharomyces cerevisiae - cytology | Saccharomyces cerevisiae - metabolism | Gene Deletion | Saccharomyces cerevisiae Proteins - metabolism | Index Medicus
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The international journal of biochemistry & cell biology, ISSN 1357-2725, 04/2014, Volume 49, Issue 1, pp. 105 - 111
Oxidative stress | Idebenone | EPI-743 | Coenzyme Q10 | Mitochondrial respiratory chain | Mitochondrial Diseases - drug therapy | Animals | Humans | Muscle Weakness - drug therapy | Ubiquinone - analogs & derivatives | Ubiquinone - deficiency | Ataxia - drug therapy | Ubiquinone - therapeutic use | Treatment Outcome | Molecular Structure | Ubiquinone - chemistry | Index Medicus
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Critical reviews in biochemistry and molecular biology, ISSN 1040-9238, 2/2013, Volume 48, Issue 1, pp. 69 - 88
Ubiquinone biosynthesis | metazoan model systems | COQ genes | ubiquinone deficiency | unicellular model systems | human patients | coenzyme Q | Human patients | Unicellular model systems | Coenzyme Q | Metazoan model systems | Ubiquinone deficiency | Life Sciences & Biomedicine | Biochemistry & Molecular Biology | Science & Technology | Mitochondrial Diseases - genetics | Humans | Ubiquinone - deficiency | Mitochondrial Diseases - metabolism | Ubiquinone - metabolism | Ubiquinone - genetics | Muscle Weakness - genetics | Phenotype | Animals | Muscle Weakness - metabolism | Mutation | Ataxia - genetics | Ataxia - metabolism | Ubiquinone - chemistry | Index Medicus | ubiquinone biosynthesis
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Locking loop movement in the ubiquinone pocket of complex I disengages the proton pumps
Nature communications, ISSN 2041-1723, 2018, Volume 9, Issue 1, pp. 4500 - 10
Science & Technology - Other Topics | Multidisciplinary Sciences | Science & Technology | Electron Transport | Mutagenesis, Site-Directed | Reactive Oxygen Species - metabolism | Yarrowia - metabolism | Proton Pumps - chemistry | Disulfides | Models, Molecular | Crystallography, X-Ray | Proton Pumps - ultrastructure | Molecular Dynamics Simulation | Mitochondrial Membranes - metabolism | Electron Transport Complex I - chemistry | Electron Transport Complex I - genetics | Escherichia coli - genetics | Escherichia coli - metabolism | Escherichia coli Proteins - genetics | Electron Transport Complex I - ultrastructure | Protein Conformation | Mitochondrial Membranes - enzymology | Enzyme Activation | Kinetics | Ubiquinone - ultrastructure | Ubiquinone - chemistry | Yarrowia - genetics | Protons | Binding | NADH-ubiquinone oxidoreductase | Reactive oxygen species | Disulfide bonds | Oxidoreductase | Electron transfer | Proteins | Electron transport chain | Mitochondria | Ubiquinone | NADH | Mutagenesis | Pumping | Site-directed mutagenesis | Energy conversion | Nicotinamide adenine dinucleotide | Ubiquinone oxidoreductase | Index Medicus
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Trends in cell biology, ISSN 0962-8924, 2016, Volume 26, Issue 5, pp. 367 - 378
Pathology | ubiquinone | electron transport | mitochondria | reactive oxygen species | coenzyme Q | Coenzyme Q | Mitochondria | Reactive oxygen species | Ubiquinone | Electron transport | Life Sciences & Biomedicine | Science & Technology | Cell Biology | Animals | Reactive Oxygen Species - metabolism | Energy Metabolism | Signal Transduction | Antioxidants - metabolism | Humans | Ubiquinone - metabolism | Mitochondria - metabolism | Ubiquinone - chemistry | Ubiquinone - biosynthesis | Enzymes | Genetic engineering | Index Medicus
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