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BBA - Molecular and Cell Biology of Lipids, ISSN 1388-1981, 03/2020, Volume 1865, Issue 3, p. 158596
The mitochondrial phospholipid (CL) has been linked to mitochondrial and cellular functions. It has been postulated that the composition of CL is of impact for... 
Tafazzin | Fatty acid supplementation | Proliferation | Cardiolipin | Glioma cells
Journal Article
Circulation Journal, ISSN 1346-9843, 2018
Background: Left ventricular non-compaction (LVNC) is a cardiomyopathy morphologically characterized by 2-layered myocardium and numerous prominent... 
Cardiomyopathy | Tafazzin (TAZ) | Left ventricular non-compaction
Journal Article
Journal Article
Autophagy, ISSN 1554-8627, 04/2015, Volume 11, Issue 4, pp. 643 - 652
Tafazzin (TAZ) is a phospholipid transacylase that catalyzes the remodeling of cardiolipin, a mitochondrial phospholipid required for oxidative... 
TLCL, tetralinoleoyl-cardiolipin | mitochondrial dysfunction | MLCL, monolysocardiolipin | BafA1, bafilomycin A | BTHS, Barth syndrome | Barth syndrome | mitophagosome | CCCP, carbonyl cyanide m-chlorophenylhydrazone | PARK2, parkin RBR E3 ubiquitin protein ligase | MAP1LC3B/LC3B, microtubule-associated protein 1 light chain 3 beta | TAZ, tafazzin | LTG, LysoTracker Green | autophagy | FCCP, carbonyl cyanide p-triflouromethoxyphenylhydrazone | PINK1, PTEN-induced putative kinase 1 | CL, cardiolipin | AdGFP-LC3, recombinant adenovirus expressing GFP tagged MAP1LC3B | AdTAZ, recombinant adenovirus expressing Myc-tagged TAZ | cardiolipin | tafazzin | 1 | mitophagy | MEF, mouse embryonic fibroblast | MTR, MitoTracker Red | SOD2, superoxide dismutase 2 mitochondrial | Dox, doxycycline | Tafazzin | Mitochondrial dysfunction | Mitophagosome | Cardiolipin | Mitophagy | Autophagy | RESPIRATORY-CHAIN | OXIDATIVE STRESS | FUSION | STABILITY | CARDIOMYOPATHY | BARTH-SYNDROME | CARDIAC-MUSCLE | MITOCHONDRIAL-MEMBRANE | CELL BIOLOGY | SKELETAL-MUSCLE | DISEASE | Cardiomyopathy, Dilated - genetics | Cardiomyopathy, Dilated - pathology | Humans | Transcription Factors - deficiency | Autophagy - physiology | Cardiolipins - metabolism | Transcription Factors - genetics | Mutation - genetics | Cardiomyopathy, Dilated - metabolism | Mitochondrial Degradation - physiology | Transcription Factors - metabolism | Animals | Mitochondria - genetics | Mice | Autophagy - genetics
Journal Article
BBA - Molecular and Cell Biology of Lipids, ISSN 1388-1981, 03/2013, Volume 1831, Issue 3, pp. 582 - 588
Cardiolipin, the specific phospholipid of mitochondria, is involved in the biogenesis, the dynamics, and the supramolecular organization of mitochondrial... 
Mitochondrion | Molecular species | Tafazzin | Thermodynamics | Cardiolipin | MUTANT | OXIDATIVE STRESS | BIOCHEMISTRY & MOLECULAR BIOLOGY | BARTH-SYNDROME | MODEL | CELL BIOLOGY | ACYLTRANSFERASE | BIOPHYSICS | MITOCHONDRIAL PHOSPHATIDYLETHANOLAMINE | GENE | LYMPHOBLAST MITOCHONDRIA | MUTATIONS | ALCAT1 | Lipids | Mitochondrial DNA
Journal Article
Cardiovascular and Hematological Disorders - Drug Targets, ISSN 1871-529X, 2014, Volume 14, Issue 2, pp. 98 - 106
Journal Article
Journal of Korean Medical Science, ISSN 1011-8934, 05/2013, Volume 28, Issue 5, pp. 784 - 787
Journal Article
JOURNAL OF LIPID RESEARCH, ISSN 0022-2275, 08/2008, Volume 49, Issue 8, pp. 1607 - 1620
In this article, the formation of prokaryotic and eukaryotic cardiolipin is reviewed in light of its biological function. I begin with a detailed account of... 
RESPIRATORY-CHAIN | POLYMORPHIC PHASE-BEHAVIOR | BIOCHEMISTRY & MOLECULAR BIOLOGY | ESCHERICHIA-COLI | BARTH-SYNDROME | phospholipids | CARRIER PROTEIN | RAT-LIVER MITOCHONDRIA | PHOSPHOLIPID SCRAMBLASE-3 | mitochondrial biogenesis | tafazzin | TETRALINOLEOYL-CARDIOLIPIN | BACILLUS-SUBTILIS | molecular species | CYTOCHROME-C RELEASE | Thematic Review
Journal Article
Mitochondrion, ISSN 1567-7249, 3/2015, Volume 21, pp. 27 - 32
Tafazzin is a transacylase that affects cardiolipin fatty acid composition and mitochondrial function. Mutations in human tafazzin cause Barth syndrome yet the... 
Tafazzin | Protein complex | Membrane assembly | Barth syndrome | Mitochondria | Cardiolipin
Journal Article
International Journal of Hematology-Oncology and Stem Cell Research, ISSN 2008-3009, 4/2018, Volume 12, Issue 2, pp. 153 - 165
Tafazzin (TAZ) protein has been upregulated in various types of human cancers, although the basis for elevation is uncertain, it has been made definite that... 
Tafazzin | Proteoglycan | Stemness | Extracellular matrix | Original | Oncoprotein
Journal Article
BBA - Molecular and Cell Biology of Lipids, ISSN 1388-1981, 04/2019, Volume 1864, Issue 4, pp. 452 - 465
The mitochondrial phospholipid cardiolipin (CL) has been implicated with mitochondrial morphology, function and, more recently, with cellular proliferation.... 
Cell proliferation | Tafazzin | CRISPR-Cas | Cardiolipin | BIOCHEMISTRY & MOLECULAR BIOLOGY | BARTH SYNDROME | CELL BIOLOGY | ELECTRON-TRANSPORT CHAIN | BIOPHYSICS | METABOLISM | GROWTH | PROGRESSION | LIPIDS | Glucose metabolism | Membrane lipids | Gliomas | Fatty acids
Journal Article
Frontiers in Genetics, ISSN 1664-8021, 2016, Volume 6, p. 359
Mutations in the gene encoding the enzyme tafazzin, TAZ, cause Barth syndrome (BTHS). Individuals with this X-linked multisystem disorder present... 
Tafazzin | Barth syndrome | Mitochondria | Stem cells | Mitochondrially targeted antioxidant | Cardiolipin | Cellular models | Reactive oxygen species | Gene mutations | Genetic aspects | Observations | Health aspects | Stem Cells | Barth Syndrome | Cellular Models | cardiolipin
Journal Article
The application of clinical genetics, ISSN 1178-704X, 2019, Volume 12, pp. 95 - 106
Barth syndrome is an ultra-rare, infantile-onset, X-linked recessive mitochondrial disorder, primarily affecting males, due to variants in encoding for the... 
X-linked | Barth syndrome | non-compaction | TAZ | cardiomyopathy | tafazzin
Journal Article
Journal of biological chemistry, ISSN 0021-9258, 2011, Volume 286, Issue 2, pp. 899 - 908
Journal Article
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, ISSN 0027-8424, 02/2009, Volume 106, Issue 7, pp. 2337 - 2341
Quantitative and qualitative alterations of mitochondrial cardiolipin have been implicated in the pathogenesis of Barth syndrome, an X-linked cardioskeletal... 
APOPTOSIS | DROSOPHILA-MELANOGASTER | Drosophila | MULTIDISCIPLINARY SCIENCES | MODEL | PLA2G6 | cardiolipin | INFANTILE NEUROAXONAL DYSTROPHY | tafazzin | METABOLISM | BIOSYNTHESIS | iPLA2 | CARDIOLIPIN DEFICIENCY | DIFFERENTIATION | LINKED CARDIOSKELETAL MYOPATHY | Care and treatment | Cardiomyopathy | Development and progression | Cardiolipin | Research | Health aspects | Heart diseases | Risk factors
Journal Article